ANAESTHETIC MANAGEMENT OF A PATIENT WITH HOMOCYSTINURIA

被引：2
作者：
Gogate, Vandana [1 ]
Nag, Kusha [1 ]
Kedareshwar [1 ]
Sanikop, C. S. [1 ]
Singh, Naveen [1 ]
机构：
[1] Jawaharlal Nehru Med Coll, Dept Anaesthesiol, Belgaum, Karnataka, India
来源：
SRI LANKAN JOURNAL OF ANAESTHESIOLOGY | 2010年 / 18卷 / 02期
关键词：
homocystinuria; thromboembolism; hypoglycemia; general anaesthesia; homocysteine metabolism;
D O I：
10.4038/slja.v18i2.1463
中图分类号：
R614 [麻醉学];
学科分类号：
100217 ;
摘要：
Homocystinuria is an autosomal recessive disease with multiple systemic involvement. Extracapsular extraction of lens is the most commonly performed elective ocular procedure for homocystinuric children. These children present with particular anaesthetic concerns during surgery. Here we report a case of a 14 year old boy with homocystinuria posted for extracapsular lens extraction under general anaesthesia. Precautions were taken perioperatively to prevent the various complications associated with this condition for a favourable perioperative outcome.
引用
收藏
页码：84 / 86
页数：3
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