ANESTHETIC MANAGEMENT IN EPIDERMOLYSIS-BULLOSA - REVIEW OF 129 ANESTHETIC EPISODES IN 32 PATIENTS

被引:18
作者
LIN, AN
LATEEF, F
KELLY, R
ROTHAUS, KO
CARTER, DM
机构
[1] NEW YORK HOSP,CORNELL MED COLL,DEPT ANESTHESIOL,NEW YORK,NY
[2] NEW YORK HOSP,CORNELL MED COLL,DEPT SURG,NEW YORK,NY
[3] HOSP SPECIAL SURG,NEW YORK,NY
关键词
D O I
10.1016/S0190-9622(94)70048-6
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Background: Anesthestic and monitoring instrumentations such as endotracheal intubation may cause skin and mucosal damage with potentially serious consequences in patients with epidermolysis bullosa (EB). Objective: This study defines the risks of skin and mucosal damage from anesthetic and monitoring techniques in patients with EB and formulates management guidelines. Methods: We retrospectively analyzed the outcome of 129 anesthetic episodes in 32 patients with various types of EB. Results: Serious complications did not occur in any patient with EB from the use of endotracheal intubation, face mask, nerve blocks, local anesthetics, and intravenous or intramuscular anesthetic agents. Conclusion: With appropriate precautions, patients with EB can undergo standard anesthetic techniques with only minor and infrequent complications.
引用
收藏
页码:412 / 416
页数:5
相关论文
共 36 条
[1]  
BERRYHILL RE, 1978, ANESTH ANALG, V57, P281
[2]   JUNCTIONAL EPIDERMOLYSIS-BULLOSA OF THE LARYNX - REPORT OF A CASE AND LITERATURE-REVIEW [J].
BERSON, S ;
WARD, RF ;
LIN, AN ;
CARTER, DM .
ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, 1992, 101 (10) :861-865
[3]   EPIDERMOLYSIS BULLOSA - A REVIEW OF 15 YEARS EXPERIENCE, INCLUDING EXPERIENCE WITH COMBINED GENERAL AND REGIONAL ANESTHETIC TECHNIQUES [J].
BOUGHTON, R ;
CRAWFORD, MR ;
VONWILLER, JB .
ANAESTHESIA AND INTENSIVE CARE, 1988, 16 (03) :260-264
[4]  
BROSTER T, 1987, ANESTH ANALG, V66, P341
[5]   PORPHYRIA WITH EPIDERMOLYSIS BULLOSA - REPORT OF A CASE OF THE TARDIVE CONGENITAL TYPE WITH DEMONSTRATION OF LATENT PORPHYRIA IN A SISTER OF THE PATIENT [J].
BRUNSTING, LA ;
MASON, HL .
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1946, 132 (09) :509-514
[6]   AUTOSOMAL RECESSIVE EPIDERMOLYSIS BULLOSA SIMPLEX - GENERALIZED PHENOTYPIC FEATURES SUGGESTIVE OF JUNCTIONAL OR DYSTROPHIC EPIDERMOLYSIS BULLOSA, AND ASSOCIATION WITH NEUROMUSCULAR DISEASES [J].
FINE, JD ;
STENN, J ;
JOHNSON, L ;
WRIGHT, T ;
BOCK, HGO ;
HORIGUCHI, Y .
ARCHIVES OF DERMATOLOGY, 1989, 125 (07) :931-938
[7]  
Fisk G C, 1973, Anaesth Intensive Care, V1, P297
[8]   ANESTHETIC MANAGEMENT IN PATIENTS WITH EPIDERMOLYSIS BULLOSA DYSTROPHICA [J].
HAGEN, R ;
LANGENBERG, C .
ANAESTHESIA, 1988, 43 (06) :482-485
[9]   ANESTHETIC MANAGEMENT OF A PATIENT WITH EPIDERMOLYSIS BULLOSA DYSTROPHICA [J].
HAMANN, RA ;
COHEN, PJ .
ANESTHESIOLOGY, 1971, 34 (04) :389-&
[10]   EXTRACUTANEOUS EPITHELIAL INVOLVEMENT IN INHERITED EPIDERMOLYSIS BULLOSA [J].
HOLBROOK, KA .
ARCHIVES OF DERMATOLOGY, 1988, 124 (05) :726-731