THE LARGE SUBUNIT OF PORCINE INNER MITOCHONDRIAL MEMBRANE-BOUND BETA-OXIDATION COMPLEX IS A LONG-CHAIN ENOYL-COA HYDRATASE - 3-HYDROXYACYL-COA DEHYDROGENASE BIFUNCTIONAL ENZYME

被引:0
|
作者
YANG, SY [1 ]
机构
[1] NEW YORK STATE INST BASIC RES DEV DISABIL, STATEN ISL, NY 10314 USA
来源
FASEB JOURNAL | 1994年 / 8卷 / 07期
关键词
D O I
暂无
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:A1348 / A1348
页数:1
相关论文
共 46 条
  • [21] Acute respiratory distress syndrome in long-chain 3-hydroxyacyl-CoA dehydrogenase and mitochondrial trifunctional protein deficiencies
    Lundy, CT
    Shield, JPH
    Kvittingen, EA
    Vinorum, OJ
    Trimble, ER
    Morris, AAM
    JOURNAL OF INHERITED METABOLIC DISEASE, 2003, 26 (06) : 537 - 541
  • [22] CDNA CLONING OF THE HUMAN PEROXISOMAL ENOYL-COA HYDRATASE - 3-HYDROXYACYL-COA DEHYDROGENASE BIFUNCTIONAL ENZYME AND LOCALIZATION TO CHROMOSOME 3Q26.3-3Q28 - A FREE LEFT ALU ARM IS INSERTED IN THE 3' NONCODING REGION
    HOEFLER, G
    FORSTNER, M
    MCGUINNESS, MC
    HULLA, W
    HIDEN, M
    KRISPER, P
    KENNER, L
    RIED, T
    LENGAUER, C
    ZECHNER, R
    MOSER, HW
    CHEN, GL
    GENOMICS, 1994, 19 (01) : 60 - 67
  • [23] MOLECULAR-CLONING AND SEQUENCE-ANALYSIS OF THE CDNA FOR RAT MITOCHONDRIAL ENOYL-COA HYDRATASE - STRUCTURAL AND EVOLUTIONARY RELATIONSHIPS LINKED TO THE BIFUNCTIONAL ENZYME OF THE PEROXISOMAL BETA-OXIDATION SYSTEM
    MINAMIISHII, N
    TAKETANI, S
    OSUMI, T
    HASHIMOTO, T
    EUROPEAN JOURNAL OF BIOCHEMISTRY, 1989, 185 (01): : 73 - 78
  • [24] NOVEL FATTY-ACID BETA-OXIDATION ENZYMES IN RAT-LIVER MITOCHONDRIA .2. PURIFICATION AND PROPERTIES OF ENOYL-COENZYME-A (COA) HYDRATASE/3-HYDROXYACYL-COA DEHYDROGENASE/3-KETOACYL-COA THIOLASE TRIFUNCTIONAL PROTEIN
    UCHIDA, Y
    IZAI, K
    ORII, T
    HASHIMOTO, T
    JOURNAL OF BIOLOGICAL CHEMISTRY, 1992, 267 (02) : 1034 - 1041
  • [25] Acylcarnitines in fibroblasts of patients with long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency and other fatty acid oxidation disorders
    Shen, JJ
    Matern, D
    Millington, DS
    Hillman, S
    Feezor, MD
    Bennett, MJ
    Qumsiyeh, M
    Kahler, SG
    Chen, YT
    Van Hove, JLK
    JOURNAL OF INHERITED METABOLIC DISEASE, 2000, 23 (01) : 27 - 44
  • [26] INVOLVEMENT OF THE PEROXISOMAL BIFUNCTIONAL ENZYME HYDRATASE DEHYDROGENASE IN THE VERY LONG-CHAIN FATTY-ACID BETA-OXIDATION
    CAIRA, F
    CHERKAOUI, M
    LATRUFFE, MN
    M S-MEDECINE SCIENCES, 1995, 11 (08): : 1131 - 1139
  • [27] Fatal pitfalls in newborn screening for mitochondrial trifunctional protein (MTP)/long-chain 3-Hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency
    Amelie S. Lotz-Havla
    Wulf Röschinger
    Katharina Schiergens
    Katharina Singer
    Daniela Karall
    Vassiliki Konstantopoulou
    Saskia B. Wortmann
    Esther M. Maier
    Orphanet Journal of Rare Diseases, 13
  • [28] Fatal pitfalls in newborn screening for mitochondrial trifunctional protein (MTP)/long-chain 3-Hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency
    Lotz-Havla, Amelie S.
    Roeschinger, Wulf
    Schiergens, Katharina
    Singer, Katharina
    Karall, Daniela
    Konstantopoulou, Vassiliki
    Wortmann, Saskia B.
    Maier, Esther M.
    ORPHANET JOURNAL OF RARE DISEASES, 2018, 13
  • [29] The peroxisome proliferator response element of the gene encoding the peroxisomal β-oxidation enzyme enoyl-CoA hydratase/3-hydroxyacyl-CoA dehydrogenase is a target for constitutive androstane receptor β/9-cis-retinoic acid receptor-mediated transactivation
    Kassam, A
    Winrow, CJ
    Fernandez-Rachubinski, F
    Capone, JP
    Rachubinski, RA
    JOURNAL OF BIOLOGICAL CHEMISTRY, 2000, 275 (06) : 4345 - 4350
  • [30] Respiratory chain complex I deficiency presenting with clinical and biochemical features of long-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency.
    Enns, GM
    Bennett, MJ
    Weisiger, K
    Ohnstad, C
    Golabi, M
    JOURNAL OF INVESTIGATIVE MEDICINE, 1998, 46 (01) : 86A - 86A