BENEFICIAL EFFECTS OF PENICILLAMINE TREATMENT ON HEREDITARY AVIAN MUSCULAR-DYSTROPHY

被引:43
作者
CHOU, T
HILL, EJ
BARTLE, E
WOOLLEY, K
LEQUIRE, V
OLSON, W
ROELOFS, R
PARK, JH
机构
[1] VANDERBILT UNIV,MED SCH,NEUROMUSCULAR DIS CTR,NASHVILLE,TN 37232
[2] VANDERBILT UNIV,MED SCH,DEPT PHYSIOL,NASHVILLE,TN 37232
[3] VANDERBILT UNIV,MED SCH,DEPT PATHOL,NASHVILLE,TN 37232
关键词
D O I
10.1172/JCI108163
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:842 / 849
页数:8
相关论文
共 20 条
[1]  
APOSHIAN H V, 1959, Biochem Pharmacol, V3, P38, DOI 10.1016/0006-2952(59)90006-1
[2]   EFFECTS OF SELECTED CHELATING-AGENTS AND METALS ON STABILITY OF LIVER LYSOSOMES [J].
CHVAPIL, M ;
BRADA, Z ;
RYAN, JN .
BIOCHEMICAL PHARMACOLOGY, 1972, 21 (08) :1097-&
[3]  
CORI GT, 1945, J BIOL CHEM, V159, P565
[4]   TISSUE SULFHYDRYL GROUPS [J].
ELLMAN, GL .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1959, 82 (01) :70-77
[5]  
FARRELL PM, 1966, ANN NY ACAD SCI, V138, P102
[6]   FORMATION OF LIPID PEROXIDE UNDER CONDITIONS WHICH LEAD TO SWELLING AND LYSIS OF RAT LIVER MITOCHONDRIA [J].
HOFFSTEN, PE ;
WEINSTEIN, J ;
HUNTER, FE ;
GEBICKI, JM .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1962, 7 (04) :276-&
[7]  
Julian L, 1963, MUSCULAR DYSTROPHY M, P457
[8]   NEW STEP IN TRANSMITTER RELEASE AT MYONEURAL JUNCTION [J].
KOSOWER, EM ;
WERMAN, R .
NATURE-NEW BIOLOGY, 1971, 233 (38) :121-&
[9]   EFFECT OF THIOLS IN BIOLOGICAL SYSTEMS ON PROTEIN SULFHYDRYL CONTENT [J].
LORBER, A ;
CHANG, CC ;
MASUOKA, D ;
MEACHAM, I .
BIOCHEMICAL PHARMACOLOGY, 1970, 19 (05) :1551-&
[10]  
MAHOWALD TA, 1962, J BIOL CHEM, V237, P1535