COLONIC INVOLVEMENT IN FABRYS-DISEASE

被引：21

作者：

JACK, CIA ^{[1
]}

MORRIS, AI ^{[1
]}

NASMYTH, DG ^{[1
]}

CARROLL, N ^{[1
]}

机构：

[1] ROYAL LIVERPOOL HOSP,LIVERPOOL L7 8XP,MERSEYSIDE,ENGLAND

来源：

POSTGRADUATE MEDICAL JOURNAL | 1991年 / 67卷 / 788期

关键词：

D O I：

10.1136/pgmj.67.788.584

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

The case of a 54 year old man with Fabry's disease and extensive jejunal and colonic diverticulosis causing colonic stricture is presented. Histological examination of the resected colon revealed evidence of ceramide trihexose deposition in the myenteric nerve plexus. Colonic involvement in Fabry's disease has not been reported before.

引用

页码：584 / 585

页数：2

共 6 条

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