IDENTIFICATION OF SPECIFIC SUBUNITS OF HIGHLY PURIFIED BOVINE LIVER BRANCHED-CHAIN KETOACID DEHYDROGENASE

被引:72
作者
HEFFELFINGER, SC [1 ]
SEWELL, ET [1 ]
DANNER, DJ [1 ]
机构
[1] EMORY UNIV,DEPT PEDIAT,DIV MED GENET,ATLANTA,GA 30322
关键词
D O I
10.1021/bi00293a011
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:5519 / 5522
页数:4
相关论文
共 18 条
[1]  
BLEILE DM, 1981, J BIOL CHEM, V256, P514
[2]  
BRADFORD MM, 1976, ANAL BIOCHEM, V72, P248, DOI 10.1016/0003-2697(76)90527-3
[3]   STABILIZATION OF MAMMALIAN LIVER BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE BY THIAMIN PYROPHOSPHATE [J].
DANNER, DJ ;
LEMMON, SK ;
ELSAS, LJ .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1980, 202 (01) :23-28
[4]  
DANNER DJ, 1979, J BIOL CHEM, V254, P5522
[5]   SUBCELLULAR-DISTRIBUTION AND COFACTOR FUNCTION OF HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE IN NORMAL AND MUTANT CULTURED SKIN FIBROBLASTS [J].
DANNER, DJ ;
ELSAS, LJ .
BIOCHEMICAL MEDICINE, 1975, 13 (01) :7-22
[6]  
ELSAS LJ, 1972, METAB CLIN EXP, V23, P569
[7]   ANTIBODIES TO BOVINE LIVER BRANCHED-CHAIN 2-OXO ACID DEHYDROGENASE CROSS-REACT WITH THIS ENZYME COMPLEX FROM OTHER TISSUES AND SPECIES [J].
HEFFELFINGER, SC ;
SEWELL, ET ;
DANNER, DJ .
BIOCHEMICAL JOURNAL, 1983, 213 (02) :339-344
[8]  
IDE S, 1976, J BIOL CHEM, V242, P54
[9]   BIOCHEMICAL-PROPERTIES OF MAMMALIAN 2-OXO ACID DEHYDROGENASE MULTI-ENZYME COMPLEXES AND CLINICAL RELEVANCY WITH CHRONIC LACTIC-ACIDOSIS [J].
KOIKE, M ;
KOIKE, K .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1982, 378 (MAR) :225-235
[10]   LIMITED PROTEOLYSIS OF 2-OXOGLUTARATE DEHYDROGENASE MULTI-ENZYME COMPLEX FROM BOVINE KIDNEY [J].
KRESZE, GB ;
RONFT, H ;
DIETL, B ;
STEBER, L .
FEBS LETTERS, 1981, 127 (01) :157-160