DECREASED GANGLIOSIDE NEURAMINIDASE ACTIVITY IN FIBROBLASTS FROM MUCOPOLYSACCHARIDOSIS PATIENTS - INHIBITION OF THE ACTIVITY INVITRO BY SULFATED GLYCOSAMINOGLYCANS AND OTHER COMPOUNDS

被引：37

作者：

BAUMKOTTER, J ^{[1
]}

CANTZ, M ^{[1
]}

机构：

[1] UNIV HEIDELBERG,DEPT PATHOCHEM & GEN NEUROCHEM,D-6900 HEIDELBERG,FED REP GER

来源：

BIOCHIMICA ET BIOPHYSICA ACTA | 1983年 / 761卷 / 02期

关键词：

D O I：

10.1016/0304-4165(83)90225-8

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：163 / 170

页数：8

共 29 条

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[7]

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[8] OLIGOSACCHARIDE AND GANGLIOSIDE NEURAMINIDASE ACTIVITIES OF MUCOLIPIDOSIS-I (SIALIDOSIS) AND MUCOLIPIDOSIS-II (I-CELL DISEASE) FIBROBLASTS [J].

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[9]

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