INVESTIGATION OF METABOLIC PATTERN IN MAPLE SYRUP URINE DISEASE BY MEANS OF GLASS CAPILLARY GAS-CHROMATOGRAPHY AND MASS-SPECTROMETRY

被引：48

作者：

JAKOBS, C

SOLEM, E

EK, J

HALVORSEN, K

JELLUM, E

机构：

[1] RIKS HOSP OSLO,INST CLIN BIOCHEM,OSLO,NORWAY

[2] RIKS HOSP OSLO,DEPT PEDIAT,OSLO,NORWAY

[3] AKERSHUS CENT HOSP,NORDBYHAGEN,NORWAY

来源：

JOURNAL OF CHROMATOGRAPHY | 1977年 / 143卷 / 01期

关键词：

D O I：

10.1016/S0378-4347(00)81324-9

中图分类号：

O65 [分析化学];

学科分类号：

070302 ; 081704 ;

摘要：

引用

页码：31 / 38

页数：8

共 16 条

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[8] BRANCHED-CHAIN ALPHA-KETO ACIDS ISOLATED AS OXIME DERIVATIVES - RELATIONSHIP TO CORRESPONDING HYDROXY-ACIDS AND AMINO-ACIDS IN MAPLE SYRUP URINE DISEASE [J].

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[9] INCREASED URINARY-EXCRETION OF 3-HYDROXYISOVALERIC ACID IN PATIENTS WITH KETOACIDOSIS [J].

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[10] ACCUMULATION OF 3-HYDROXYISOBUTYRIC ACID, 2-METHYL-3-HYDROXYBUTYRIC ACID AND 3-HYDROXYISOVALERIC ACID IN KETOACIDOSIS [J].

LANDAAS, S .

CLINICA CHIMICA ACTA, 1975, 64 (02) :143-154

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