NEUROIMAGING STUDY OF MYOTONIC-DYSTROPHY .2. MRI MEASUREMENTS OF THE BRAIN

被引:11
作者
HASHIMOTO, T
TAYAMA, M
MIYAZAKI, M
MURAKAWA, K
KAWAI, H
NISHITANI, H
KURODA, Y
机构
[1] UNIV TOKUSHIMA,SCH MED,DEPT INTERNAL MED,TOKUSHIMA,JAPAN
[2] UNIV TOKUSHIMA,SCH MED,DEPT RADIOL,TOKUSHIMA 770,JAPAN
关键词
MYOTONIC DYSTROPHY; MAGNETIC RESONANCE IMAGING; BRAIN MEASUREMENT; PENS; CORPUS CALLOSUM;
D O I
10.1016/0387-7604(94)00097-H
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The brain of patients with adult type myotonic dystrophy was measured using MRT, and compared with age- and sex-matched controls, The width of the cerebrum, and the areas of the corpus callosum, pens and pituitary gland were significantly smaller in adult-type myotonic dystrophy than in the controls, The IQ of the patients with adult-type myotonic dystrophy was lower than that of controls, These results demonstrate a decreased volume of the brain and pituitary glands in myotonic dystrophy, These findings suggest a causal relationship for the mental retardation and endocrine dysfunction that may occur.
引用
收藏
页码:28 / 32
页数:5
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