EXPRESSION OF A MYELIN BASIC-PROTEIN GENE IN TRANSGENIC SHIVERER MICE - CORRECTION OF THE DYSMYELINATING PHENOTYPE

被引:320
|
作者
READHEAD, C
POPKO, B
TAKAHASHI, N
SHINE, HD
SAAVEDRA, RA
SIDMAN, RL
HOOD, L
机构
[1] HARVARD UNIV,CHILDRENS HOSP,SCH MED,DEPT NEUROPATHOL,BOSTON,MA 02115
[2] HARVARD UNIV,CHILDRENS HOSP,SCH MED,DEPT NEUROSCI,BOSTON,MA 02115
关键词
D O I
10.1016/0092-8674(87)90248-0
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:703 / 712
页数:10
相关论文
共 50 条
  • [21] EXPRESSION OF A NOVEL TRANSCRIPT OF THE MYELIN BASIC-PROTEIN GENE
    KITAMURA, K
    NEWMAN, SL
    CAMPAGNONI, CW
    VERDI, JM
    MOHANDAS, T
    HANDLEY, VW
    CAMPAGNONI, AT
    JOURNAL OF NEUROCHEMISTRY, 1990, 54 (06) : 2032 - 2041
  • [22] CELL AND TISSUE-SPECIFIC EXPRESSION OF A HETEROLOGOUS GENE UNDER CONTROL OF THE MYELIN BASIC-PROTEIN GENE PROMOTER IN TRANSGENIC MICE
    MISKIMINS, R
    KNAPP, L
    DEWEY, MJ
    ZHANG, XP
    DEVELOPMENTAL BRAIN RESEARCH, 1992, 65 (02): : 217 - 221
  • [23] MYELIN DEFICIENT MICE - EXPRESSION OF MYELIN BASIC-PROTEIN AND GENERATION OF MICE WITH VARYING LEVELS OF MYELIN
    POPKO, B
    PUCKETT, C
    LAI, E
    SHINE, HD
    READHEAD, C
    TAKAHASHI, N
    HUNT, SW
    SIDMAN, RL
    HOOD, L
    CELL, 1987, 48 (04) : 713 - 721
  • [24] COMPACT MYELIN EXISTS IN THE ABSENCE OF BASIC-PROTEIN IN THE SHIVERER MUTANT MOUSE
    KIRSCHNER, DA
    GANSER, AL
    NATURE, 1980, 283 (5743) : 207 - 210
  • [25] THE EFFECT OF THE SHIVERER MUTATION ON MYELIN BASIC-PROTEIN EXPRESSION IN HOMOZYGOUS AND HETEROZYGOUS MOUSE-BRAIN
    BARBARESE, E
    NIELSON, ML
    CARSON, JH
    JOURNAL OF NEUROCHEMISTRY, 1983, 40 (06) : 1680 - 1686
  • [26] Myelin proteolipid protein expression in shiverer mice
    Duchala, CS
    Hays, L
    Macklin, WB
    JOURNAL OF NEUROCHEMISTRY, 1996, 66 : S84 - S84
  • [27] MYELIN BASIC-PROTEIN GENE-EXPRESSION IN QUAKING, JIMPY, AND MYELIN SYNTHESIS-DEFICIENT MICE
    CARNOW, TB
    CARSON, JH
    BROSTOFF, SW
    HOGAN, EL
    DEVELOPMENTAL BIOLOGY, 1984, 106 (01) : 38 - 44
  • [28] MYELIN BASIC-PROTEIN DEPOSITION IN THE OPTIC AND SCIATIC-NERVES OF DYSMYELINATING MUTANTS QUAKING, JIMPY, TREMBLER, MLD, AND SHIVERER DURING DEVELOPMENT
    JACQUE, C
    DELASSALLE, A
    RAOUL, M
    BAUMANN, N
    JOURNAL OF NEUROCHEMISTRY, 1983, 41 (05) : 1335 - 1340
  • [29] MYELIN PROTEIN EXPRESSION IN NORMAL AND DYSMYELINATING MUTANT MICE
    SORG, BJA
    AGRAWAL, D
    AGRAWAL, HC
    CAMPAGNONI, AT
    FEDERATION PROCEEDINGS, 1985, 44 (04) : 1067 - 1067
  • [30] IMMUNOCHEMICAL STUDIES OF MYELIN BASIC-PROTEIN IN SHIVERER MOUSE DEVOID OF MAJOR DENSE LINE OF MYELIN
    DUPOUEY, P
    JACQUE, C
    BOURRE, JM
    CESSELIN, F
    PRIVAT, A
    BAUMANN, N
    NEUROSCIENCE LETTERS, 1979, 12 (01) : 113 - 118