FAMILIAL AMYLOIDOTIC POLYNEUROPATHY

被引:110
作者
BENSON, MD [1 ]
机构
[1] RICHARD L ROUDEBUSH VET ADM MED CTR,INDIANAPOLIS,IN 46202
关键词
D O I
10.1016/0166-2236(89)90162-8
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
引用
收藏
页码:88 / 92
页数:5
相关论文
共 31 条
[2]   HEREDITARY AMYLOIDOSIS [J].
ANDRADE, C ;
ARAKI, S ;
BLOCK, WD ;
COHEN, AS ;
JACKSON, CE ;
KUROIWA, Y ;
MCKUSICK, VA ;
NISSIM, J ;
SOHAR, E ;
VANALLEN, MW .
ARTHRITIS AND RHEUMATISM, 1970, 13 (06) :902-&
[3]   HEREDITARY AMYLOIDOSIS - DESCRIPTION OF A NEW AMERICAN KINDRED WITH LATE ONSET CARDIOMYOPATHY - APPALACHIAN AMYLOID [J].
BENSON, MD ;
WALLACE, MR ;
TEJADA, E ;
BAUMANN, H ;
PAGE, B .
ARTHRITIS AND RHEUMATISM, 1987, 30 (02) :195-200
[4]  
BENSON MD, 1975, LANCET, V1, P10
[5]  
BENSON MD, 1988, METABOLIC BASIS INHE, P3647
[6]   STRUCTURE OF HUMAN PLASMA PREALBUMIN AT 2.5 A RESOLUTION - PRELIMINARY REPORT ON POLYPEPTIDE-CHAIN CONFORMATION, QUATERNARY STRUCTURE AND THYROXINE BINDING [J].
BLAKE, CCF ;
GEISOW, MJ ;
SWAN, IDA .
JOURNAL OF MOLECULAR BIOLOGY, 1974, 88 (01) :1-&
[7]   AMYLOID FIBRIL IN HEREDITARY CEREBRAL-HEMORRHAGE WITH AMYLOIDOSIS (HCHWA) IS RELATED TO THE GASTROENTERO-PANCREATIC NEUROENDOCRINE PROTEIN, GAMMA TRACE [J].
COHEN, DH ;
FEINER, H ;
JENSSON, O ;
FRANGIONE, B .
JOURNAL OF EXPERIMENTAL MEDICINE, 1983, 158 (02) :623-628
[8]   HIGH-LEVELS OF MESSENGER-RNA FOR TRANSTHYRETIN (PREALBUMIN) IN HUMAN CHOROID-PLEXUS [J].
DICKSON, PW ;
SCHREIBER, G .
NEUROSCIENCE LETTERS, 1986, 66 (03) :311-315
[9]   PRIMARY STRUCTURE OF AN AMYLOID PREALBUMIN AND ITS PLASMA PRECURSOR IN A HEREDOFAMILIAL POLYNEUROPATHY OF SWEDISH ORIGIN [J].
DWULET, FE ;
BENSON, MD .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1984, 81 (03) :694-698
[10]   CHARACTERIZATION OF A TRANSTHYRETIN (PREALBUMIN) VARIANT ASSOCIATED WITH FAMILIAL AMYLOIDOTIC POLYNEUROPATHY TYPE-II (INDIANA SWISS) [J].
DWULET, FE ;
BENSON, MD .
JOURNAL OF CLINICAL INVESTIGATION, 1986, 78 (04) :880-886