Acquired renal cystic disease is an entity which is characterized by the progressive substitution of the atrophic renal parenchyma by multiple cysts in patients with renal insufficiency. Its main complications are hemorrhage and tumorous degeneration. The case discussed is a 57-year-old patient with terminal renal insufficiency secondary to interstitial nephropathy, who, following 6 years of treatment with hemodialysis and renal transplantation, developed a state of persistent hematuria requiring nephrectomy of the left kidney. Histological study revealed multiple cysts of monostratified epithelium with intracavitary projections, multiform adenomas and multifocal malignant tumorous polymorphism. The patient died in a state of progressive cachexia with pleural and hepatic metastasis.
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Tottori Univ, Fac Med, Dept Microbiol & Pathol, Div Organ Pathol, Tottori 6838503, JapanTottori Univ, Fac Med, Dept Microbiol & Pathol, Div Organ Pathol, Tottori 6838503, Japan
Nishihara, Keisuke
Shomori, Kohei
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Tottori Univ, Fac Med, Dept Microbiol & Pathol, Div Organ Pathol, Tottori 6838503, JapanTottori Univ, Fac Med, Dept Microbiol & Pathol, Div Organ Pathol, Tottori 6838503, Japan
Shomori, Kohei
Nagashima, Yoji
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Yokohama City Univ, Grad Sch Med, Dept Mol Pathol, Yokohama, Kanagawa 232, JapanTottori Univ, Fac Med, Dept Microbiol & Pathol, Div Organ Pathol, Tottori 6838503, Japan
Nagashima, Yoji
Kuroda, Naoto
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Kochi Red Cross Hosp, Dept Pathol & Lab Med, Kochi, JapanTottori Univ, Fac Med, Dept Microbiol & Pathol, Div Organ Pathol, Tottori 6838503, Japan
Kuroda, Naoto
Nagamatsu, Hirotaka
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Shobara Red Cross Hosp, Dept Urol, Shobara, JapanTottori Univ, Fac Med, Dept Microbiol & Pathol, Div Organ Pathol, Tottori 6838503, Japan
Nagamatsu, Hirotaka
Ito, Hisao
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Tottori Univ, Fac Med, Dept Microbiol & Pathol, Div Organ Pathol, Tottori 6838503, JapanTottori Univ, Fac Med, Dept Microbiol & Pathol, Div Organ Pathol, Tottori 6838503, Japan