THE BIOCHEMICAL BASIS OF THE BEHAVIORAL-DISORDER IN THE LESCH-NYHAN SYNDROME

被引:55
作者
BAUMEISTER, AA [1 ]
FRYE, GD [1 ]
机构
[1] TEXAS A&M UNIV,COLL MED,DEPT MED PHARMACOL & TOXICOL,COLLEGE STN,TX 77843
关键词
D O I
10.1016/0149-7634(85)90043-0
中图分类号
B84 [心理学]; C [社会科学总论]; Q98 [人类学];
学科分类号
03 ; 0303 ; 030303 ; 04 ; 0402 ;
摘要
引用
收藏
页码:169 / 178
页数:10
相关论文
共 144 条
[1]  
ADAMS A, 1971, BIOCHEM J, V125, pP36
[2]   DEVELOPMENTAL-CHANGES IN PURINE PHOSPHORIBOSYLTRANSFERASES IN HUMAN AND RAT TISSUES [J].
ADAMS, A ;
HARKNESS, RA .
BIOCHEMICAL JOURNAL, 1976, 160 (03) :565-576
[3]   SPECIES DISTRIBUTION OF XANTHINE OXIDASE [J].
ALKHALIDI, UA ;
CHAGLASSIAN, TH .
BIOCHEMICAL JOURNAL, 1965, 97 (01) :318-+
[4]   ACTIVITIES OF AMIDOPHOSPHORIBOSYLTRANSFERASE (EC2.4.2.14) AND THE PURINE PHOSPHORIBOSYLTRANSFERASES (EC2.4.2.7 AND 2.4.2.8), AND THE PHOSPHORIBOSYLPYROPHOSPHATE CONTENT OF RAT CENTRAL NERVOUS-SYSTEM AT DIFFERENT STAGES OF DEVELOPMENT - THEIR POSSIBLE RELATIONSHIP TO THE NEUROLOGICAL DYSFUNCTION IN THE LESCH-NYHAN SYNDROME [J].
ALLSOP, J ;
WATTS, RWE .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1980, 46 (02) :221-232
[5]   EVIDENCE FOR A CENTRAL NORADRENALINE RECEPTOR STIMULATION BY CLONIDINE [J].
ANDEN, NE ;
CORRODI, H ;
FUXE, K ;
HOKFELT, B ;
HOKFELT, T ;
RYDIN, C ;
SVENSSON, T .
LIFE SCIENCE PART 1 PHYSIOLOGY & PHARMACOLOGY, 1970, 9 (09) :513-&
[6]   FURTHER OBSERVATIONS ON USE OF 5-HYDROXYTRYPTOPHAN IN A CHILD WITH LESCH-NYHAN SYNDROME [J].
ANDERS, TF ;
CANN, HM ;
CIARANELLO, RD ;
BARCHAS, JD ;
BERGER, PA .
NEUROPADIATRIE, 1978, 9 (02) :157-166
[7]   EFFECT OF L-5-HYDROXYTRYPTOPHAN ON SELF-MUTILATION IN LESCH-NYHAN DISEASE - NEGATIVE REPORT [J].
ANDERSON, LT ;
HERRMANN, L ;
DANCIS, J .
NEUROPADIATRIE, 1976, 7 (04) :439-442
[8]   UTILIZATION OF PURINES BY AN HPRT VARIANT IN AN INTELLIGENT, NONMUTILATIVE PATIENT WITH FEATURES OF THE LESCH-NYHAN SYNDROME [J].
BAKAY, B ;
NISSINEN, E ;
SWEETMAN, L ;
FRANCKE, U ;
NYHAN, WL .
PEDIATRIC RESEARCH, 1979, 13 (12) :1365-1370
[9]   THE BASAL GANGLIA IN EXTRAPYRAMIDAL DYSFUNCTION [J].
BARNES, CD .
BRAIN RESEARCH BULLETIN, 1983, 11 (02) :271-275
[10]   SELF-INJURIOUS-BEHAVIOR IN RATS PRODUCED BY INTRANIGRAL MICROINJECTION OF GABA AGONISTS [J].
BAUMEISTER, AA ;
FRYE, GD .
PHARMACOLOGY BIOCHEMISTRY AND BEHAVIOR, 1984, 21 (01) :89-95