CORNEAL PERFORATION AS A COMPLICATION OF EPIDERMOLYSIS-BULLOSA ACQUISITA

Epidermolysis bullosa acquisita (EBA) is now recognised asa histopathologically distinct condition.(1-3) Ocular complications of hereditary epidermolysis bullosa (EB) have been well documented,(4) but little has been reported with respect to the ocular manifestations associated with the acquired form.(5-8) A patient with EBA and sarcoidosis - an association that does not appear to have been previously reported - developed spontaneous peripheral corneal melting and perforation. The defect healed with the use of a bandage contact lens, antibiotics, mydriatics and pulsed intravenous steroids, and resulted in a satisfactory visual outcome.