GLOBOID-CELL LEUKODYSTROPHY IS A GENERALIZED GALACTOSYL-SPHINGOSINE (PSYCHOSINE) STORAGE DISEASE

被引：55

作者：

KOBAYASHI, T

SHINODA, H

GOTO, I

YAMANAKA, T

SUZUKI, Y

机构：

[1] YAIZU MUNICIPAL GEN HOSP,DEPT PEDIAT,YAIZU 425,JAPAN

[2] NATL CTR NEUROL & PSYCHIAT,DIV INHERITED METAB DIS,KODAIRA 187,JAPAN

来源：

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1987年 / 144卷 / 01期

关键词：

D O I：

10.1016/S0006-291X(87)80472-2

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：41 / 46

页数：6

共 16 条

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[8] THE TWITCHER MOUSE - AN ENZYMATICALLY AUTHENTIC MODEL OF HUMAN GLOBOID-CELL LEUKODYSTROPHY (KRABBE DISEASE) [J].

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