CYSTIC-FIBROSIS - A DISEASE OF ION CHANNELS

被引:102
作者
FRIZZELL, RA
机构
关键词
D O I
10.1016/0166-2236(87)90144-5
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
引用
收藏
页码:190 / 193
页数:4
相关论文
共 34 条
[1]   AN ANION-SELECTIVE CHANNEL FROM THE PSEUDOMONAS-AERUGINOSA OUTER-MEMBRANE [J].
BENZ, R ;
GIMPLE, M ;
POOLE, K ;
HANCOCK, REW .
BIOCHIMICA ET BIOPHYSICA ACTA, 1983, 730 (02) :387-390
[2]   SINGLE VOLTAGE-DEPENDENT CHLORIDE-SELECTIVE CHANNELS OF LARGE CONDUCTANCE IN CULTURED RAT MUSCLE [J].
BLATZ, AL ;
MAGLEBY, KL .
BIOPHYSICAL JOURNAL, 1983, 43 (02) :237-241
[3]   SINGLE CHLORIDE-SELECTIVE CHANNELS ACTIVE AT RESTING MEMBRANE-POTENTIALS IN CULTURED RAT SKELETAL-MUSCLE [J].
BLATZ, AL ;
MAGLEBY, KL .
BIOPHYSICAL JOURNAL, 1985, 47 (01) :119-123
[4]   NA+ TRANSPORT IN CYSTIC-FIBROSIS RESPIRATORY EPITHELIA - ABNORMAL BASAL RATE AND RESPONSE TO ADENYLATE-CYCLASE ACTIVATION [J].
BOUCHER, RC ;
STUTTS, MJ ;
KNOWLES, MR ;
CANTLEY, L ;
GATZY, JT .
JOURNAL OF CLINICAL INVESTIGATION, 1986, 78 (05) :1245-1252
[5]   DETECTION OF K+ AND CL- CHANNELS FROM CALF CARDIAC SARCOLEMMA IN PLANAR LIPID BILAYER-MEMBRANES [J].
CORONADO, R ;
LATORRE, R .
NATURE, 1982, 298 (5877) :849-852
[6]   CALCIUM-DEPENDENT CHLORIDE CURRENTS IN ISOLATED CELLS FROM RAT LACRIMAL GLANDS [J].
EVANS, MG ;
MARTY, A .
JOURNAL OF PHYSIOLOGY-LONDON, 1986, 378 :437-460
[7]   SODIUM-COUPLED CHLORIDE TRANSPORT BY EPITHELIAL TISSUES [J].
FRIZZELL, RA ;
FIELD, AM ;
SCHULTZ, SG .
AMERICAN JOURNAL OF PHYSIOLOGY, 1979, 236 (01) :F1-F8
[8]   ALTERED REGULATION OF AIRWAY EPITHELIAL-CELL CHLORIDE CHANNELS IN CYSTIC-FIBROSIS [J].
FRIZZELL, RA ;
RECHKEMMER, G ;
SHOEMAKER, RL .
SCIENCE, 1986, 233 (4763) :558-560
[9]   SINGLE CL- CHANNELS IN MOLLUSCAN NEURONS - MULTIPLICITY OF THE CONDUCTANCE STATES [J].
GELETYUK, VI ;
KAZACHENKO, VN .
JOURNAL OF MEMBRANE BIOLOGY, 1985, 86 (01) :9-15
[10]   CL--CHANNELS IN THE APICAL CELL-MEMBRANE OF THE RECTAL GLAND INDUCED BY CAMP [J].
GREGER, R ;
SCHLATTER, E ;
GOGELEIN, H .
PFLUGERS ARCHIV-EUROPEAN JOURNAL OF PHYSIOLOGY, 1985, 403 (04) :446-448