HUMAN-LIVER N-ACETYLGLUCOSAMINE-6-SULFATE SULFATASE - CATALYTIC PROPERTIES

被引:31
作者
FREEMAN, C [1 ]
HOPWOOD, JJ [1 ]
机构
[1] ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,KING WILLIAM RD,N ADELAIDE,SA 5006,AUSTRALIA
关键词
D O I
10.1042/bj2460355
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:355 / 365
页数:11
相关论文
共 37 条
[1]  
BASNER R, 1979, J BIOL CHEM, V254, P1151
[2]   HUMAN ALPHA-L-IDURONIDASE .2. CATALYTIC PROPERTIES [J].
CLEMENTS, PR ;
MULLER, V ;
HOPWOOD, JJ .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1985, 152 (01) :29-34
[3]  
DIXON M, 1964, ENZYMES, P75
[4]   DETECTION OF THE SANFILIPPO-D SYNDROME BY THE USE OF A RADIOLABELED MONOSACCHARIDE SULFATE AS THE SUBSTRATE FOR THE ESTIMATION OF N-ACETYLGLUCOSAMINE-6-SULFATE SULFATASE [J].
ELLIOTT, H ;
HOPWOOD, JJ .
ANALYTICAL BIOCHEMISTRY, 1984, 138 (01) :205-209
[5]  
FRANSSON LA, 1980, EUR J BIOCHEM, V106, P59
[6]   HUMAN-LIVER N-ACETYLGLUCOSAMINE-6-SULFATE SULFATASE - PURIFICATION AND CHARACTERIZATION [J].
FREEMAN, C ;
CLEMENTS, PR ;
HOPWOOD, JJ .
BIOCHEMICAL JOURNAL, 1987, 246 (02) :347-354
[7]   HUMAN-LIVER SULFAMATE SULFOHYDROLASE - DETERMINATIONS OF NATIVE PROTEIN AND SUBUNIT MR VALUES AND INFLUENCE OF SUBSTRATE AGYLCONE STRUCTURE ON CATALYTIC PROPERTIES [J].
FREEMAN, C ;
HOPWOOD, JJ .
BIOCHEMICAL JOURNAL, 1986, 234 (01) :83-92
[8]   INTRALYSOSOMAL FORMATION AND METABOLIC-FATE OF N-ACETYLGLUCOSAMINE 6-SULFATE FROM KERATAN SULFATE [J].
FUCHS, W ;
BECK, M ;
KRESSE, H .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1985, 151 (03) :551-556
[9]   MOLECULAR DISTINCTIONS BETWEEN HEPARAN-SULFATE AND HEPARIN - ANALYSIS OF SULFATION PATTERNS INDICATES THAT HEPARAN-SULFATE AND HEPARIN ARE SEPARATE FAMILIES OF N-SULFATED POLYSACCHARIDES [J].
GALLAGHER, JT ;
WALKER, A .
BIOCHEMICAL JOURNAL, 1985, 230 (03) :665-674
[10]  
HABUCHI H, 1979, J BIOL CHEM, V254, P7570