Treatable chorea associated with polycythemia vera

被引：0

作者：

Miyagawa, Toji ^{[1
]}

Ueda, Koki ^{[2
]}

Ohtomo, Ryo ^{[1
]}

Sasaki, Takuya ^{[1
]}

Takahashi, Miwako ^{[3
]}

Momose, Toshimitsu ^{[3
]}

Kurokawa, Mineo ^{[2
,4
]}

Tsuji, Shoji ^{[1
]}

机构：

[1] Univ Tokyo Hosp, Grad Sch Med, Dept Neurol, Tokyo, Japan

[2] Univ Tokyo Hosp, Grad Sch Med, Dept Hematol & Oncol, Tokyo, Japan

[3] Univ Tokyo Hosp, Grad Sch Med, Dept Radiol, Tokyo, Japan

[4] Univ Tokyo Hosp, Dept Cell Therapy & Transplantat Med, Tokyo, Japan

来源：

NEUROLOGY AND CLINICAL NEUROSCIENCE | 2014年 / 2卷 / 03期

关键词：

chorea; elderly women; JAK2 V617F mutation; phlebotomy; polycythemia vera;

D O I：

10.1111/ncn3.94

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

We report a case of a 70-year-old woman with polycythemia vera and 5 years of persistent generalized chorea. Despite the long duration of the choreic condition, it completely resolved after the normalization of the hematocrit by serial phlebotomies. Diffuse cerebral hypoperfusion evaluated by 99m Tc-hexamethyl-propylene amine oxime (HMPAO) single-photon emission computed tomography (SPECT) improved in accordance with the intensive hematocrit control. We recommend an increased awareness of this rare, but treatable cause of chorea in elderly patients.

引用

页码：90 / 91

页数：2

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