NEGRO VARIETY OF HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN IS A MILD FORM OF THALASSEMIA

被引:27
作者
CHARACHE, S
CLEGG, JB
WEATHERALL, DJ
机构
[1] JOHNS HOPKINS UNIV HOSP,DEPT HEMATOL,BALTIMORE,MD 21205
[2] UNIV OXFORD,RADCLIFFE INFIRM,NUFFIELD COLL,DEPT CLIN MED,OXFORD OX2 6HE,ENGLAND
关键词
D O I
10.1111/j.1365-2141.1976.tb03599.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:527 / 534
页数:8
相关论文
共 40 条
[1]  
ADAMSON JW, 1975, SEMIN HEMATOL, V12, P383
[2]   OBSERVATIONS ON THE CHROMATOGRAPHIC HETEROGENEITY OF NORMAL ADULT AND FETAL HUMAN HEMOGLOBIN - A STUDY OF THE EFFECTS OF CRYSTALLIZATION AND CHROMATOGRAPHY ON THE HETEROGENEITY AND ISOLEUCINE CONTENT [J].
ALLEN, DW ;
SCHROEDER, WA ;
BALOG, J .
JOURNAL OF THE AMERICAN CHEMICAL SOCIETY, 1958, 80 (07) :1628-1634
[3]   OXYGEN BOHR EFFECT OF HUMAN FETAL HEMOGLOBIN [J].
ANTONINI, E ;
FRONTICELLI, C ;
REICHLIN, M ;
BRUNORI, M ;
FANELLI, AR ;
BUCCI, E ;
WYMAN, J .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1964, 108 (03) :569-&
[4]  
ANTONINI E, 1972, OXYGEN AFFINITY HEMO, P121
[5]   INTERACTION OF 2,3-DIPHOSPHOGLYCERATE WITH VARIOUS HUMAN HEMOGLOBINS [J].
BUNN, HF ;
BRIEHL, RW .
JOURNAL OF CLINICAL INVESTIGATION, 1970, 49 (06) :1088-&
[6]   IMBALANCED GLOBIN CHAIN SYNTHESIS IN HETEROZYGOUS BETA-THALASSEMIC BONE-MARROW [J].
CHALEVELAKIS, G ;
CLEGG, JB ;
WEATHERALL, DJ .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1975, 72 (10) :3853-3857
[7]   HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN [J].
CHARACHE, S ;
CONLEY, CL .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1969, 165 (A1) :37-&
[8]   THALASSEMIA IN BLACK AMERICANS [J].
CHARACHE, S ;
CONLEY, CL ;
DOEBLIN, TD ;
BARTALOS, M .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1974, 232 (MAY24) :125-134
[9]   ABNORMAL HUMAN HAEMOGLOBINS - SEPARATION AND CHARACTERIZATION OF ALPHA AND BETA CHAINS BY CHROMATOGRAPHY AND DETERMINATION OF 2 NEW VARIANTS HB CHESAPEAKE AND HB J (BANGKOK) [J].
CLEGG, JB ;
NAUGHTON, MA ;
WEATHERA.DJ .
JOURNAL OF MOLECULAR BIOLOGY, 1966, 19 (01) :91-&
[10]   HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN - A STUDY OF 79 AFFECTED PERSONS IN 15 NEGRO FAMILIES IN BALTIMORE [J].
CONLEY, CL ;
CHARACHE, S ;
WEATHERALL, DJ ;
SHEPARD, MK ;
RICHARDSON, SN .
BLOOD, 1963, 21 (03) :261-+