THIAMINE INCREASES SPECIFIC ACTIVITY OF HUMAN LIVER BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE

被引:26
作者
DANNER, DJ
DAVIDSON, ED
ELSAS, LJ
机构
[1] EMORY UNIV,SCH MED,DEPT PEDIAT,DIV MED GENET,ATLANTA,GA 30322
[2] EMORY UNIV,SCH MED,DEPT SURG,ATLANTA,GA 30322
关键词
D O I
10.1038/254529a0
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:529 / 530
页数:2
相关论文
共 9 条
[1]   MAPLE SYRUP URINE DISEASE [J].
DANCIS, J ;
LEVITZ, ML ;
MILLER, S ;
WESTALL, RG .
BMJ-BRITISH MEDICAL JOURNAL, 1959, 1 (JAN10) :91-93
[2]   STUDIES IN MAPLE SYRUP URINE DISEASE [J].
DENT, CE ;
WESTALL, RG .
ARCHIVES OF DISEASE IN CHILDHOOD, 1961, 36 (187) :259-+
[3]   CLASSICAL MAPLE SYRUP URINE DISEASE - COFACTOR RESISTANCE [J].
ELSAS, LJ ;
WHEELER, FB ;
TRUSLER, S ;
PERL, DP ;
PASK, BA .
METABOLISM-CLINICAL AND EXPERIMENTAL, 1972, 21 (10) :929-&
[4]   MAPLE SYRUP URINE DISEASE - COENZYME FUNCTION AND PRENATAL MONITORING [J].
ELSAS, LJ ;
PRIEST, JH ;
WHEELER, FB ;
DANNER, DJ ;
PASK, BA .
METABOLISM-CLINICAL AND EXPERIMENTAL, 1974, 23 (06) :569-579
[5]  
ELSAS LJ, US JAPAN C THIAMINE
[6]  
MENKES JH, 1954, PEDIATRICS, V14, P462
[7]   HOMOCYSTINURIA DUE TO CYSTATHIONINE SYNTHASE DEFICIENCY - EFFECT OF PYRIDOXINE [J].
MUDD, SH ;
EDWARDS, WA ;
LOEB, PM ;
BROWN, MS ;
LASTER, L .
JOURNAL OF CLINICAL INVESTIGATION, 1970, 49 (09) :1762-+
[8]  
SCRIVER CR, 1971, LANCET, V1, P310
[9]  
WONG PWK, 1972, CLIN GENET, V3, P27