HOMOCYSTINURIA DUE TO CYSTATHIONINE SYNTHASE DEFICIENCY - METABOLISM OF L-METHIONINE

被引:69
作者
LASTER, L
MUDD, SH
FINKELSTEIN, JD
IRREVERRE, F
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关键词
D O I
10.1172/JCI105278
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
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页码:1708 / +
页数:1
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共 28 条
[21]  
Mueller JH, 1923, J BIOL CHEM, V58, P373
[22]  
ORR ML, 1957, 4 US DEP AGR HOM EC
[23]   AUTOMATIC RECORDING APPARATUS FOR USE IN THE CHROMATOGRAPHY OF AMINO ACIDS [J].
SPACKMAN, DH ;
STEIN, WH ;
MOORE, S .
ANALYTICAL CHEMISTRY, 1958, 30 (07) :1190-1206
[24]  
SPAETH GL, IN PRESS
[25]  
STEIN WH, 1954, J BIOL CHEM, V211, P915
[26]   THE DETECTION OF THE KETO ACIDS OF PLANTS - A PROCEDURE BASED ON THEIR CONVERSION TO AMINO ACIDS [J].
TOWERS, GHN ;
THOMPSON, JF ;
STEWARD, FC .
JOURNAL OF THE AMERICAN CHEMICAL SOCIETY, 1954, 76 (09) :2392-2396
[27]  
YOUNG L, 1958, METABOLISM SULPHUR C, P59
[28]  
1961, REPORT COMMITTEE ENZ, P127