Thoracoscopic Pericardiectomy for Constrictive Pericarditis in a Pediatric Patient With Mulibrey Nanism

被引：1

作者：

Christov, Georgi ^{[1
]}

Burch, Michael ^{[1
]}

Andrews, Rachel ^{[1
]}

Hurst, Jane ^{[2
]}

Ashworth, Michael ^{[3
]}

Mustafa, Muhammad ^{[4
]}

Muthialu, Nagarajan ^{[4
]}

机构：

[1] Great Ormond St Hosp Sick Children, Dept Cardiol, Cardiothorac Unit, London, England

[2] Great Ormond St Hosp Sick Children, Dept Clin Genet, Cardiothorac Unit, London, England

[3] Great Ormond St Hosp Sick Children, Dept Pathol, Cardiothorac Unit, London, England

[4] Great Ormond St Hosp Sick Children, Dept Cardiothorac Surg, Cardiothorac Unit, London, England

来源：

WORLD JOURNAL FOR PEDIATRIC AND CONGENITAL HEART SURGERY | 2013年 / 4卷 / 04期

关键词：

pericardiectomy; thoracoscopy; mulibrey nanism;

D O I：

10.1177/2150135113485761

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Mulibrey nanism is a rare autosomal recessive disease with multisystem involvement. Clinical deterioration is most often related to cardiac involvement in the form of restrictive or constrictive disorders, and pericardiectomy may be required. We report a case of Mulibrey nanism in a patient of non-Finnish origin, where a thoracoscopic pericardiectomy helped in good palliation and clinical recovery.

引用

页码：442 / 443

页数：2

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