CERVICOMEDULLARY JUNCTION DECOMPRESSION IN A CASE OF MARSHALL-SMITH SYNDROME - CASE-REPORT

被引:9
作者
PAPPAS, CTE [1 ]
REKATE, HL [1 ]
机构
[1] BARROW NEUROL INST, DIV NEUROL SURG, 350 W THOMAS RD, PHOENIX, AZ 85013 USA
关键词
CERVICOMEDULLARY JUNCTION; MARSHALL-SMITH SYNDROME; SPINAL CANAL COMPRESSION;
D O I
10.3171/jns.1991.75.2.0317
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The case is reported of a 2-year-old boy born with Marshall-Smith syndrome who had difficulty in swallowing and who exhibited spasticity and quadriparesis due to compression of the medulla and cervical spine. This is the first child with this rare condition reported to have brain-stem compression from bone abnormalities at the craniovertebral junction and who has required surgery.
引用
收藏
页码:317 / 319
页数:3
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