SEZARY-SYNDROME IN AN 11-YEAR-OLD GIRL

被引:24
作者
MEISTER, L
DUARTE, AM
DAVIS, J
PEREZ, JL
SCHACHNER, LA
机构
[1] UNIV MIAMI,SCH MED,DEPT DERMATOL & CUTANEOUS SURG,POB 016250 R250,MIAMI,FL 33101
[2] UNIV MIAMI,SCH MED,DEPT PEDIAT,MIAMI,FL 33101
[3] UNIV MIAMI,SCH MED,DEPT PATHOL,MIAMI,FL 33101
关键词
D O I
10.1016/0190-9622(93)70017-N
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
All forms of cutaneous T-cell lymphoma are rare in children. We describe an 11-year-old girl who had generalized exfoliative erythroderma, intense pruritus, peripheral lymphadenopathy, mycosis cells in the skin and lymph nodes, and Sezary cells in the peripheral blood. Results of a biopsy specimen of involved skin showed changes consistent with mycosis fungoides. A classic case of Sezary syndrome has not previously been reported in childhood or pre-adolescence.
引用
收藏
页码:93 / 95
页数:3
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