NECROTIZING SARCOID GRANULOMATOSIS - A SERIES OF 4 CASES

被引:0
作者
SDOUN, D
KAMBOUCHNER, M
TAZI, A
LATTAIGNANT, JC
MARGENT, P
ARONDELLE, C
CARVAILLO, D
GROUSSARD, O
BATTESTI, JP
机构
[1] CTR HOSP BEAUVAIS,SERV PNEUMOL,F-60000 BEAUVAIS,FRANCE
[2] HOP AVICENNE,SERV ANAT PATHOL,F-93009 BOBIGNY,FRANCE
[3] HOP DELAFONTAINE 2,SERV MED INTERNE,F-93205 ST DENIS,FRANCE
[4] HOP BEAUJON,SERV ANAT PATHOL,F-92210 CLICHY,FRANCE
来源
ANNALES DE MEDECINE INTERNE | 1994年 / 145卷 / 04期
关键词
SARCOIDOSIS; NECROTIZING GRANULOMATOSIS; VASCULITIS;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Necrotizing sarcoid granulomatosis (NSG) was first described by Liebow in 1973 among the heading << pulmonary angeitis and granulomatosis >>. We reported four cases of NSG. The diagnostic was made by open lung biopsy in all, and the distinctive features were those described by Liebow : presence of numerous sarcoid-like granulomas, foci of fibrinoid necrosis and granulomatous vasculitis. Clinical, radiological, and clinical course characteristics allow the reasonable conclusion that NSG is the histopathological substratum of a variety of sarcoidosis affections termed << nodular sarcoidosis >>.
引用
收藏
页码:230 / 233
页数:4
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