PREPONDERANCE OF LYSOSOMAL BODIES IN CULTURED FIBROBLASTS FROM PATIENTS WITH RECESSIVE EPIDERMOLYSIS BULLOSA DYSTROPHICA - ELECTRON-MICROSCOPIC STUDY

被引:5
作者
KANAN, MW
FRANCIS, MJO
SYKES, B
REED, WB
RYAN, TJ
VANDIEST, P
MARSDEN, A
机构
[1] UNIV OXFORD,DEPT HUMAN ANAT,OXFORD,ENGLAND
[2] UNIV OXFORD,NUFFIELD DEPT ORTHOPAED SURG,OXFORD,ENGLAND
[3] UNIV CALIF IRVINE,IRVINE,CA 92664
[4] UNITED OXFORD HOSP,DEPT DERMATOL,OXFORD,ENGLAND
关键词
D O I
10.1111/j.1365-2133.1977.tb07156.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
引用
收藏
页码:521 / 531
页数:11
相关论文
共 30 条
[1]  
BARTON RW, 1971, J BIOL CHEM, V246, P7773
[2]   DISTINCT BIOCHEMICAL DEFICIT IN MAROTEAUX-LAMY SYNDROME (MUCOPOLYSACCHARIDOSIS VI) [J].
BARTON, RW ;
NEUFELD, EF .
JOURNAL OF PEDIATRICS, 1972, 80 (01) :114-+
[3]  
BAUER EA, 1974, CLIN RES, V22, pA326
[4]   FORMATION AND ORIGIN OF BASAL LAMINA AND ANCHORING FIBRILS IN ADULT HUMAN SKIN [J].
BRIGGAMAN, RA ;
DALLDORF, FG ;
WHEELER, CE .
JOURNAL OF CELL BIOLOGY, 1971, 51 (02) :384-+
[5]   EPIDERMOLYSIS BULLOSA DYSTROPHICA RECESSIVE - POSSIBLE ROLE OF ANCHORING FIBRILS IN PATHOGENESIS [J].
BRIGGAMAN, RA ;
WHEELER, CE .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1975, 65 (02) :203-211
[6]  
BRIGGAMAN RA, 1973, EPIDERMOLYSIS BULLOS
[7]   COMPARATIVE ULTRASTRUCTURE OF CHICK FIBROBLASTS IN-VITRO AT EARLY AND LATE STAGES DURING THEIR GROWTH SPAN [J].
BROCK, MA ;
HAY, RJ .
JOURNAL OF ULTRASTRUCTURE RESEARCH, 1971, 36 (3-4) :291-+
[8]   ULTRASTRUCTURAL LOCALIZATION OF ACID PHOSPHATASE ALKALINE PHOSPHATASE AND ADENOSINE TRIPHOSPHATASE IN INDUCED GOITRES OF XENOPUS LAEVIS DAUDIN TADPOLES [J].
COLEMAN, R ;
EVENNETT, PJ ;
DODD, JM .
HISTOCHEMIE, 1967, 10 (01) :33-+
[9]  
DANES BS, 1973, TISSUE CULTURE METHO, P627
[10]  
DANES BS, 1969, J EXPT MEDICINE, V129, P725