CHLORIDE AND POTASSIUM CHANNELS IN CYSTIC-FIBROSIS AIRWAY EPITHELIA

被引:380
作者
WELSH, MJ
LIEDTKE, CM
机构
[1] UNIV IOWA,COLL MED,DEPT INTERNAL MED,DIV PULM,IOWA CITY,IA 52242
[2] CASE WESTERN RESERVE UNIV,SCH MED,DEPT PEDIAT DEV GENET & ANAT,CTR CYST FIBROSIS,CLEVELAND,OH 44106
关键词
D O I
10.1038/322467a0
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:467 / 470
页数:4
相关论文
共 14 条
[1]  
ALBAZZAZ FJ, 1981, AM REV RESPIR DIS, V123, P295
[2]   IMPROVED PATCH-CLAMP TECHNIQUES FOR HIGH-RESOLUTION CURRENT RECORDING FROM CELLS AND CELL-FREE MEMBRANE PATCHES [J].
HAMILL, OP ;
MARTY, A ;
NEHER, E ;
SAKMANN, B ;
SIGWORTH, FJ .
PFLUGERS ARCHIV-EUROPEAN JOURNAL OF PHYSIOLOGY, 1981, 391 (02) :85-100
[3]   ABNORMAL ION PERMEATION THROUGH CYSTIC-FIBROSIS RESPIRATORY EPITHELIUM [J].
KNOWLES, MR ;
STUTTS, MJ ;
SPOCK, A ;
FISCHER, N ;
GATZY, JT ;
BOUCHER, RC .
SCIENCE, 1983, 221 (4615) :1067-1070
[4]  
LIEDTKE CM, 1983, AM J PHYSL, V247, pC441
[5]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[6]   CHLORIDE IMPERMEABILITY IN CYSTIC-FIBROSIS [J].
QUINTON, PM .
NATURE, 1983, 301 (5899) :421-422
[7]   DEFECTIVE BETA-ADRENERGIC RESPONSE OF CYSTIC-FIBROSIS SWEAT GLANDS INVIVO AND INVITRO [J].
SATO, K ;
SATO, F .
JOURNAL OF CLINICAL INVESTIGATION, 1984, 73 (06) :1763-1771
[8]  
SHOEMAKER RL, 1986, BIOPHYS J, V49, pA158
[9]   CHLORIDE SECRETION BY CANINE TRACHEAL EPITHELIUM .1. ROLE OF INTRACELLULAR CAMP LEVELS [J].
SMITH, PL ;
WELSH, MJ ;
STOFF, JS ;
FRIZZELL, RA .
JOURNAL OF MEMBRANE BIOLOGY, 1982, 70 (03) :217-226
[10]  
Welsh M. J., 1986, PHYSL MEMBRANE DISOR, P751