NEUROSARCOIDOSIS MASQUERADING AS GLIOMA OF THE OPTIC CHIASM IN A CHILD

被引:22
作者
NG, KL
MCDERMOTT, N
ROMANOWSKI, CAJ
JACKSON, A
机构
[1] MANCHESTER ROYAL INFIRM,DEPT NEURORADIOL,MANCHESTER M13 9WL,LANCS,ENGLAND
[2] MANCHESTER ROYAL INFIRM,DEPT NEUROL,MANCHESTER M13 9WL,LANCS,ENGLAND
关键词
NEUROSARCOIDOSIS; OPTIC GLIOMA; MAGNETIC RESONANCE IMAGING;
D O I
10.1136/pgmj.71.835.265
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We present a case of sarcoidosis in a 14-year-old girl who presented with a short history of visual disturbance. Computed tomography and magnetic resonance imaging (MRI) demonstrated enlargement of the optic chiasm and prechiasmic optic nerves. Post-contrast MRI showed marginal enhancement of the affected areas of the optic pathways. A diagnosis of optic nerve glioma and arachnoid gliomatosis was made; surgical confirmation was not sought due to the risk to vision associated with biopsy. A rapid clinical deterioration led to repeat MRI which demonstrated extensive enhancing soft tissue throughout the basal cisterns with extension into the brain. Biopsy confirmed a diagnosis of sarcoidosis.
引用
收藏
页码:265 / 268
页数:4
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