DECREASED MEMBRANE MECHANICAL STABILITY AND INVIVO LOSS OF SURFACE-AREA REFLECT SPECTRIN DEFICIENCIES IN HEREDITARY SPHEROCYTOSIS

被引：89
作者：
CHASIS, JA
AGRE, P
MOHANDAS, N
机构：
[1] UNIV CALIF SAN FRANCISCO, CANC RES INST, DEPT LAB MED, SAN FRANCISCO, CA 94143 USA
[2] JOHNS HOPKINS UNIV, SCH MED, DEPT MED, BALTIMORE, MD 21205 USA
[3] JOHNS HOPKINS UNIV, SCH MED, DEPT CELL BIOL ANAT, BALTIMORE, MD 21205 USA
来源：
JOURNAL OF CLINICAL INVESTIGATION | 1988年 / 82卷 / 02期
关键词：
D O I：
10.1172/JCI113640
中图分类号：
R-3 [医学研究方法]; R3 [基础医学];
学科分类号：
1001 ;
摘要：
引用
收藏
页码：617 / 623
页数：7
相关论文
共 28 条
[1]   INHERITANCE PATTERN AND CLINICAL-RESPONSE TO SPLENECTOMY AS A REFLECTION OF ERYTHROCYTE SPECTRIN DEFICIENCY IN HEREDITARY SPHEROCYTOSIS [J].
AGRE, P ;
ASIMOS, A ;
CASELLA, JF ;
MCMILLAN, C .
NEW ENGLAND JOURNAL OF MEDICINE, 1986, 315 (25) :1579-1583
[2]   PARTIAL DEFICIENCY OF ERYTHROCYTE SPECTRIN IN HEREDITARY SPHEROCYTOSIS [J].
AGRE, P ;
CASELLA, JF ;
ZINKHAM, WH ;
MCMILLAN, C ;
BENNETT, V .
NATURE, 1985, 314 (6009) :380-383
[3]  
BECKER PS, 1985, CLIN HAEMATOL, V14, P15
[4]   ABNORMAL OXIDANT SENSITIVITY AND BETA-CHAIN STRUCTURE OF SPECTRIN IN HEREDITARY SPHEROCYTOSIS ASSOCIATED WITH DEFECTIVE SPECTRIN-PROTEIN 4.1 BINDING [J].
BECKER, PS ;
MORROW, JS ;
LUX, SE .
JOURNAL OF CLINICAL INVESTIGATION, 1987, 80 (02) :557-565
[5]   ERYTHROCYTE-MEMBRANE RIGIDITY INDUCED BY GLYCOPHORIN-A LIGAND INTERACTION - EVIDENCE FOR A LIGAND-INDUCED ASSOCIATION BETWEEN GLYCOPHORIN-A AND SKELETAL PROTEINS [J].
CHASIS, JA ;
MOHANDAS, N ;
SHOHET, SB .
JOURNAL OF CLINICAL INVESTIGATION, 1985, 75 (06) :1919-1926
[6]   ERYTHROCYTE-MEMBRANE DEFORMABILITY AND STABILITY - 2 DISTINCT MEMBRANE-PROPERTIES THAT ARE INDEPENDENTLY REGULATED BY SKELETAL PROTEIN ASSOCIATIONS [J].
CHASIS, JA ;
MOHANDAS, N .
JOURNAL OF CELL BIOLOGY, 1986, 103 (02) :343-350
[7]  
CHASIS JA, 1987, CLIN RES, V35, pA422
[8]   OSMOTIC GRADIENT EKTACYTOMETRY - COMPREHENSIVE CHARACTERIZATION OF RED-CELL VOLUME AND SURFACE MAINTENANCE [J].
CLARK, MR ;
MOHANDAS, N ;
SHOHET, SB ;
HOESCH, RM ;
ROSSI, ME .
BLOOD, 1983, 61 (05) :899-910
[9]   PARTIAL ANKYRIN AND SPECTRIN DEFICIENCY IN SEVERE, ATYPICAL HEREDITARY SPHEROCYTOSIS [J].
COETZER, TL ;
LAWLER, J ;
LIU, SC ;
PRCHAL, JT ;
GUALTIERI, RJ ;
BRAIN, MC ;
DACIE, JV ;
PALEK, J .
NEW ENGLAND JOURNAL OF MEDICINE, 1988, 318 (04) :230-234
[10]  
COHEN AM, 1986, BLOOD, V68, P920
123