IDIOPATHIC INFANTILE ARTERIAL CALCIFICATION - A SURVIVING PATIENT WITH RENAL-ARTERY STENOSIS

被引:31
作者
THIAVILLE, A [1 ]
SMETS, A [1 ]
CLERCX, A [1 ]
PERLMUTTER, N [1 ]
机构
[1] UNIV BRUSSELS,HOP ENFANTS REINE FABIOLA,DEPT NEONATAL,B-1020 BRUSSELS,BELGIUM
关键词
D O I
10.1007/BF02015014
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Idiopathic infantile arterial calcification (IIAC) is a rare hereditary, fatal disease. Death occurs usually within the first 28 months of life. IIAC is characterized by calcifications along the internal elastic membrane and proliferation of the intimal layer of muscular arteries. Specific therapy consists of administration of diphosphantes, but its effectiveness has been a matter of controversy. We report a case treated with diphosphonates which has had an unusual outcome.
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收藏
页码:506 / 508
页数:3
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