GROUP-C NIEMANN-PICK DISEASE - FAULTY REGULATION OF LOW-DENSITY-LIPOPROTEIN UPTAKE AND CHOLESTEROL STORAGE IN CULTURED FIBROBLASTS

被引:172
作者
PENTCHEV, PG
COMLY, ME
KRUTH, HS
TOKORO, T
BUTLER, J
SOKOL, J
FILLINGKATZ, M
QUIRK, JM
MARSHALL, DC
PATEL, S
VANIER, MT
BRADY, RO
机构
[1] FAC MED LYON SUD,INSERM,U189,BIOCHIM LAB,F-69921 OULLINS,FRANCE
[2] NHLBI,EXPTL ATHEROSCLEROSIS LAB,BETHESDA,MD 20892
[3] NICHHD,HUMAN GENET BRANCH,BETHESDA,MD 20892
[4] VET ADM MED CTR,NEUROL SERV,NEWINGTON,CT 06111
关键词
D O I
10.1096/fasebj.1.1.3609608
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:40 / 45
页数:6
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