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HOMOCYSTINURIA DUE TO CYSTATHIONINE SYNTHASE DEFICIENCY - STUDIES OF NITROGEN-BALANCE AND SULFUR EXCRETION
被引:25
作者
:
POOLE, JR
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,DIGEST & HEREDITARY DIS BRANCH,BETHESDA,MD 20014
POOLE, JR
MUDD, SH
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,DIGEST & HEREDITARY DIS BRANCH,BETHESDA,MD 20014
MUDD, SH
CONERLY, EB
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,DIGEST & HEREDITARY DIS BRANCH,BETHESDA,MD 20014
CONERLY, EB
EDWARDS, WA
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,DIGEST & HEREDITARY DIS BRANCH,BETHESDA,MD 20014
EDWARDS, WA
机构
:
[1]
NIAMDD,DIGEST & HEREDITARY DIS BRANCH,BETHESDA,MD 20014
[2]
NIMH,LAB GEN & COMP BIOCHEM,BETHESDA,MD 20014
来源
:
JOURNAL OF CLINICAL INVESTIGATION
|
1975年
/ 55卷
/ 05期
关键词
:
D O I
:
10.1172/JCI108004
中图分类号
:
R-3 [医学研究方法];
R3 [基础医学];
学科分类号
:
1001 ;
摘要
:
引用
收藏
页码:1033 / 1048
页数:16
相关论文
共 56 条
[1]
BARBER GW, 1967, LANCET, V1, P337
[2]
SPECIFICITY AND SOME OTHER PROPERTIES OF LIVER SERINE SULPHHYDRASE - EVIDENCE FOR ITS IDENTITY WITH CYSTATHIONINE BETA-SYNTHASE
[J].
BRAUNSTE.AE
论文数:
0
引用数:
0
h-index:
0
BRAUNSTE.AE
;
GORYACHE.EV
论文数:
0
引用数:
0
h-index:
0
GORYACHE.EV
;
TOLOSA, EA
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0
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0
h-index:
0
TOLOSA, EA
;
WILLHARD.IH
论文数:
0
引用数:
0
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0
WILLHARD.IH
;
YEFREMOV.LL
论文数:
0
引用数:
0
h-index:
0
YEFREMOV.LL
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1971,
242
(01)
:247
-&
[3]
BRENTON DP, 1966, Q J MED, V35, P325
[4]
SWEAT AND MISCELLANEOUS NITROGEN LOSSES IN HUMAN BALANCE STUDIES
[J].
CALLOWAY, DH
论文数:
0
引用数:
0
h-index:
0
CALLOWAY, DH
;
ODELL, ACF
论文数:
0
引用数:
0
h-index:
0
ODELL, ACF
;
MARGEN, S
论文数:
0
引用数:
0
h-index:
0
MARGEN, S
.
JOURNAL OF NUTRITION,
1971,
101
(06)
:775
-&
[5]
VARIATION IN ENDOGENOUS NITROGEN EXCRETION AND DIETARY NITROGEN UTILIZATION AS DETERMINANTS OF HUMAN PROTEIN REQUIREMENT
[J].
CALLOWAY, DH
论文数:
0
引用数:
0
h-index:
0
CALLOWAY, DH
;
MARGEN, S
论文数:
0
引用数:
0
h-index:
0
MARGEN, S
.
JOURNAL OF NUTRITION,
1971,
101
(02)
:205
-&
[6]
HOMOCYSTINURIA .2. SUBNORMAL SERUM FOLATE LEVELS INCREASED FOLATE CLEARANCE AND EFFECTS OF FOLIC ACID THERAPY
[J].
CAREY, MC
论文数:
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0
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CAREY, MC
;
FENNELLY, JJ
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0
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0
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0
FENNELLY, JJ
;
FITZGERALD, O
论文数:
0
引用数:
0
h-index:
0
FITZGERALD, O
.
AMERICAN JOURNAL OF MEDICINE,
1968,
45
(01)
:26
-+
[7]
HOMOCYSTINURIA - A NEW INBORN ERROR OF METABOLISM ASSOCIATED WITH MENTAL DEFICIENCY
[J].
CARSON, NAJ
论文数:
0
引用数:
0
h-index:
0
CARSON, NAJ
;
DENT, CE
论文数:
0
引用数:
0
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0
DENT, CE
;
FIELD, CMB
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0
引用数:
0
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0
FIELD, CMB
;
NEILL, DW
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0
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0
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0
NEILL, DW
;
WESTALL, RG
论文数:
0
引用数:
0
h-index:
0
WESTALL, RG
;
CUSWORTH, DC
论文数:
0
引用数:
0
h-index:
0
CUSWORTH, DC
.
ARCHIVES OF DISEASE IN CHILDHOOD,
1963,
38
(201)
:425
-+
[8]
DETERMINATION OF CREATININE BY MEANS OF AUTOMATIC CHEMICAL ANALYSIS
[J].
CHASSON, AL
论文数:
0
引用数:
0
h-index:
0
CHASSON, AL
;
STANLEY, MA
论文数:
0
引用数:
0
h-index:
0
STANLEY, MA
;
GRADY, HJ
论文数:
0
引用数:
0
h-index:
0
GRADY, HJ
.
AMERICAN JOURNAL OF CLINICAL PATHOLOGY,
1961,
35
(01)
:83
-&
[9]
HOMOCYSTINURIA
[J].
CUSWORTH, DC
论文数:
0
引用数:
0
h-index:
0
机构:
Medical Unit, University College Hospital, London
CUSWORTH, DC
;
DENT, CE
论文数:
0
引用数:
0
h-index:
0
机构:
Medical Unit, University College Hospital, London
DENT, CE
.
BRITISH MEDICAL BULLETIN,
1969,
25
(01)
:42
-+
[10]
DEFICIENCIES OF CYSTATHIONASE AND HOMOSERINE DEHYDRATASE ACTIVITIES IN CYSTATHIONINURIA
[J].
FINKELST.JD
论文数:
0
引用数:
0
h-index:
0
FINKELST.JD
;
MUDD, SH
论文数:
0
引用数:
0
h-index:
0
MUDD, SH
;
IRREVERR.F
论文数:
0
引用数:
0
h-index:
0
IRREVERR.F
;
LASTER, L
论文数:
0
引用数:
0
h-index:
0
LASTER, L
.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1966,
55
(04)
:865
-&
←
1
2
3
4
5
6
→
共 56 条
[1]
BARBER GW, 1967, LANCET, V1, P337
[2]
SPECIFICITY AND SOME OTHER PROPERTIES OF LIVER SERINE SULPHHYDRASE - EVIDENCE FOR ITS IDENTITY WITH CYSTATHIONINE BETA-SYNTHASE
[J].
BRAUNSTE.AE
论文数:
0
引用数:
0
h-index:
0
BRAUNSTE.AE
;
GORYACHE.EV
论文数:
0
引用数:
0
h-index:
0
GORYACHE.EV
;
TOLOSA, EA
论文数:
0
引用数:
0
h-index:
0
TOLOSA, EA
;
WILLHARD.IH
论文数:
0
引用数:
0
h-index:
0
WILLHARD.IH
;
YEFREMOV.LL
论文数:
0
引用数:
0
h-index:
0
YEFREMOV.LL
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1971,
242
(01)
:247
-&
[3]
BRENTON DP, 1966, Q J MED, V35, P325
[4]
SWEAT AND MISCELLANEOUS NITROGEN LOSSES IN HUMAN BALANCE STUDIES
[J].
CALLOWAY, DH
论文数:
0
引用数:
0
h-index:
0
CALLOWAY, DH
;
ODELL, ACF
论文数:
0
引用数:
0
h-index:
0
ODELL, ACF
;
MARGEN, S
论文数:
0
引用数:
0
h-index:
0
MARGEN, S
.
JOURNAL OF NUTRITION,
1971,
101
(06)
:775
-&
[5]
VARIATION IN ENDOGENOUS NITROGEN EXCRETION AND DIETARY NITROGEN UTILIZATION AS DETERMINANTS OF HUMAN PROTEIN REQUIREMENT
[J].
CALLOWAY, DH
论文数:
0
引用数:
0
h-index:
0
CALLOWAY, DH
;
MARGEN, S
论文数:
0
引用数:
0
h-index:
0
MARGEN, S
.
JOURNAL OF NUTRITION,
1971,
101
(02)
:205
-&
[6]
HOMOCYSTINURIA .2. SUBNORMAL SERUM FOLATE LEVELS INCREASED FOLATE CLEARANCE AND EFFECTS OF FOLIC ACID THERAPY
[J].
CAREY, MC
论文数:
0
引用数:
0
h-index:
0
CAREY, MC
;
FENNELLY, JJ
论文数:
0
引用数:
0
h-index:
0
FENNELLY, JJ
;
FITZGERALD, O
论文数:
0
引用数:
0
h-index:
0
FITZGERALD, O
.
AMERICAN JOURNAL OF MEDICINE,
1968,
45
(01)
:26
-+
[7]
HOMOCYSTINURIA - A NEW INBORN ERROR OF METABOLISM ASSOCIATED WITH MENTAL DEFICIENCY
[J].
CARSON, NAJ
论文数:
0
引用数:
0
h-index:
0
CARSON, NAJ
;
DENT, CE
论文数:
0
引用数:
0
h-index:
0
DENT, CE
;
FIELD, CMB
论文数:
0
引用数:
0
h-index:
0
FIELD, CMB
;
NEILL, DW
论文数:
0
引用数:
0
h-index:
0
NEILL, DW
;
WESTALL, RG
论文数:
0
引用数:
0
h-index:
0
WESTALL, RG
;
CUSWORTH, DC
论文数:
0
引用数:
0
h-index:
0
CUSWORTH, DC
.
ARCHIVES OF DISEASE IN CHILDHOOD,
1963,
38
(201)
:425
-+
[8]
DETERMINATION OF CREATININE BY MEANS OF AUTOMATIC CHEMICAL ANALYSIS
[J].
CHASSON, AL
论文数:
0
引用数:
0
h-index:
0
CHASSON, AL
;
STANLEY, MA
论文数:
0
引用数:
0
h-index:
0
STANLEY, MA
;
GRADY, HJ
论文数:
0
引用数:
0
h-index:
0
GRADY, HJ
.
AMERICAN JOURNAL OF CLINICAL PATHOLOGY,
1961,
35
(01)
:83
-&
[9]
HOMOCYSTINURIA
[J].
CUSWORTH, DC
论文数:
0
引用数:
0
h-index:
0
机构:
Medical Unit, University College Hospital, London
CUSWORTH, DC
;
DENT, CE
论文数:
0
引用数:
0
h-index:
0
机构:
Medical Unit, University College Hospital, London
DENT, CE
.
BRITISH MEDICAL BULLETIN,
1969,
25
(01)
:42
-+
[10]
DEFICIENCIES OF CYSTATHIONASE AND HOMOSERINE DEHYDRATASE ACTIVITIES IN CYSTATHIONINURIA
[J].
FINKELST.JD
论文数:
0
引用数:
0
h-index:
0
FINKELST.JD
;
MUDD, SH
论文数:
0
引用数:
0
h-index:
0
MUDD, SH
;
IRREVERR.F
论文数:
0
引用数:
0
h-index:
0
IRREVERR.F
;
LASTER, L
论文数:
0
引用数:
0
h-index:
0
LASTER, L
.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1966,
55
(04)
:865
-&
←
1
2
3
4
5
6
→