EVIDENCE OF INHERITED UREA CYCLE DEFECT IN A CASE OF FATAL VALPROATE TOXICITY

被引:45
作者
HJELM, M
DESILVA, LVK
SEAKINS, JWT
OBERHOLZER, VG
ROLLES, CJ
机构
[1] INST CHILD HLTH,LONDON WC1N 3JH,ENGLAND
[2] SOUTHAMPTON GEN HOSP,DEPT PAEDIAT,SOUTHAMPTON SO9 4XY,HANTS,ENGLAND
关键词
D O I
10.1136/bmj.292.6512.23
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:23 / 24
页数:2
相关论文
共 5 条
[1]   DETERMINATION OF THE RATE OF UREA SYNTHESIS FROM SERIAL MEASUREMENTS OF PLASMA UREA CONCENTRATION AFTER AN ALANINE LOAD - THEORETICAL AND METHODOLOGICAL ASPECTS [J].
GEISELER, D ;
KAY, JDS ;
OBERHOLZER, VG ;
SEAKINS, JWT ;
HJELM, M .
CLINICAL SCIENCE, 1985, 68 (02) :201-208
[2]  
HARRIS ML, 1980, CLIN CHEM, V26, P473
[3]  
KAY JDS, 1984, 3RD INT S INB ERR ME, P86
[4]  
ROLLES CJ, 1983, BR J CLIN PRACT S, V27, P72
[5]   THE RENAL ORIGIN OF SODIUM VALPROATE-INDUCED HYPERAMMONEMIA IN FASTING HUMANS [J].
WARTER, JM ;
BRANDT, C ;
MARESCAUX, C ;
RUMBACH, L ;
MICHELETTI, G ;
CHABRIER, G ;
KRIEGER, J ;
IMLER, M .
NEUROLOGY, 1983, 33 (09) :1136-1140