OSTEONECTIN CONTENT IN HUMAN OSTEOGENESIS IMPERFECTA BONE SHOWS A RANGE SIMILAR TO THAT OF 2 BOVINE MODELS OF OI

被引:15
作者
FISHER, LW [1 ]
DRUM, MA [1 ]
ROBEY, PG [1 ]
CONN, KM [1 ]
TERMINE, JD [1 ]
机构
[1] NIDR, CLIN INVEST & PATIENTS CARE BRANCH, BETHESDA, MD 20892 USA
关键词
D O I
10.1007/BF02555258
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:260 / 264
页数:5
相关论文
共 31 条
  • [1] SUBTLE STRUCTURAL ALTERATIONS IN THE CHAINS OF TYPE-I PROCOLLAGEN PRODUCE OSTEOGENESIS IMPERFECTA TYPE-II
    BONADIO, J
    BYERS, PH
    [J]. NATURE, 1985, 316 (6026) : 363 - 366
  • [2] ABNORMAL ALPHA-2-CHAIN IN TYPE-I COLLAGEN FROM A PATIENT WITH A FORM OF OSTEOGENESIS IMPERFECTA
    BYERS, PH
    SHAPIRO, JR
    ROWE, DW
    DAVID, KE
    HOLBROOK, KA
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 1983, 71 (03) : 689 - 697
  • [3] INTERNAL DELETION IN A COLLAGEN GENE IN A PERINATAL LETHAL FORM OF OSTEOGENESIS IMPERFECTA
    CHU, ML
    WILLIAMS, CJ
    PEPE, G
    HIRSCH, JL
    PROCKOP, DJ
    RAMIREZ, F
    [J]. NATURE, 1983, 304 (5921) : 78 - 80
  • [4] MATRIX PROTEIN PROFILES IN CALF BONE-DEVELOPMENT
    CONN, KM
    TERMINE, JD
    [J]. BONE, 1985, 6 (01) : 33 - 36
  • [5] HERITABLE BONE FRAGILITY, JOINT LAXITY AND DYSPLASTIC DENTIN IN FRIESIAN CALVES - A BOVINE SYNDROME OF OSTEOGENESIS IMPERFECTA
    DENHOLM, LJ
    COLE, WG
    [J]. AUSTRALIAN VETERINARY JOURNAL, 1983, 60 (01) : 9 - 17
  • [6] DEVRIES WN, 1986, J BIOL CHEM, V261, P9056
  • [7] DEWET WJ, 1983, J BIOL CHEM, V258, P7721
  • [8] NUCLEASE S1 MAPPING OF A HOMOZYGOUS MUTATION IN THE CARBOXYLPROPEPTIDE-CODING REGION OF THE PRO-ALPHA-2(I) COLLAGEN GENE IN A PATIENT WITHE OSTEOGENESIS IMPERFECTA
    DICKSON, LA
    PIHLAJANIEMI, T
    DEAK, S
    POPE, FM
    NICHOLLS, A
    PROCKOP, DJ
    MYERS, JC
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1984, 81 (14): : 4524 - 4528
  • [9] FISHER LW, 1983, J BIOL CHEM, V258, P2723
  • [10] FISHER LW, 1983, J BIOL CHEM, V258, P6588