D-LACTIC ACIDURIA, AN INBORN ERROR OF METABOLISM

被引:38
作者
DURAN, M [1 ]
VANBIERVLIET, JPGM [1 ]
KAMERLING, JP [1 ]
WADMAN, SK [1 ]
机构
[1] UNIV CHILDRENS HOSP HET WILHELMINA KINDERZIEKENHUIS,UTRECHT,NETHERLANDS
关键词
D O I
10.1016/0009-8981(77)90297-2
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:297 / 300
页数:4
相关论文
共 7 条
[1]   BACTERIAL CATABOLISM OF THREONINE - THREONINE DEGRADATION INITIATED BY L-THREONINE-NAD+ OXIDOREDUCTASE [J].
BELL, SC ;
TURNER, JM .
BIOCHEMICAL JOURNAL, 1976, 156 (02) :449-458
[2]   L-THREONINE CATABOLISM VIA AMINOACETONE - SEARCH FOR A PATHWAY IN BACTERIA [J].
BELL, SC ;
TURNER, JM .
BIOCHEMICAL SOCIETY TRANSACTIONS, 1976, 4 (03) :497-500
[3]  
HOHORST HJ, 1962, METHOD ENZYMAT AN, P622
[4]  
KAMERLING JP, IN PRESS
[5]   RENAL EXCRETION OF LACTIC ACID IN EXERCISE [J].
MILLER, AT ;
MILLER, JO .
JOURNAL OF APPLIED PHYSIOLOGY, 1949, 1 (08) :614-618
[6]   ALPHA-KETOADIPIC ACIDURIA, A NEW INBORN ERROR OF LYSINE METABOLISM - BIOCHEMICAL STUDIES [J].
PRZYREMBEL, H ;
BACHMANN, D ;
LOMBECK, I ;
BECKER, K ;
WENDEL, U ;
WADMAN, SK ;
BREMER, HJ .
CLINICA CHIMICA ACTA, 1975, 58 (03) :257-269
[7]   ABNORMAL TYROSINE AND PHENYLALANINE METABOLISM IN PATIENTS WITH TYROSYLURIA AND PHENYLKETONURIA - GAS-LIQUID CHROMATOGRAPHIC ANALYSIS OF URINARY METABOLITES [J].
WADMAN, SK ;
VANDERHE.C ;
KETTING, D ;
VANSPRAN.FJ .
CLINICA CHIMICA ACTA, 1971, 34 (02) :277-&