Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS

被引:6
作者
Saladi, Lakshmi [1 ]
Roy, Swati [2 ]
Diaz-Fuentes, Gilda [1 ]
机构
[1] Icahn Sch Med Mt Sinai, Bronx Lebanon Hosp Ctr, Div Pulm & Crit Care Med, Bronx, NY 10457 USA
[2] Icahn Sch Med Mt Sinai, Dept Med, Bronx Lebanon Hosp Ctr, Bronx, NY 10457 USA
关键词
Unilateral pulmonary artery agenesis; Acute respiratory distress syndrome; Pulmonary hypertension; Pulmonary edema; Hemoptysis;
D O I
10.1016/j.rmcr.2018.02.004
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Unilateral pulmonary artery agenesis (UPAA) is a rare malformation that can present as an isolated anomaly or may be associated with certain congenital cardiac anomalies, such as tetralogy of Fallot, atrial septal defect, coarctation of aorta, right aortic arch, truncus arteriosus and pulmonary atresia. Clinical presentation is nonspecific which makes the diagnosis elusive; chronic dyspnea, hemoptysis or recurrent infections are the most common manifestations. Patients may remain asymptomatic until adulthood. There is no definitive treatment for patients with UPAA. Acute respiratory distress syndrome (ARDS) is usually a bilateral disease, unilateral ARDS has been described after lung resection or trauma. We present a case of a 39 year-old woman who developed unilateral ARDS and was later diagnosed with isolated UPAA.
引用
收藏
页码:148 / 151
页数:4
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