MORPHOLOGIC AND HISTOANATOMIC OBSERVATIONS OF THE BRAIN IN UNTREATED HUMAN PHENYLKETONURIA

被引:122
作者
BAUMAN, ML
KEMPER, TL
机构
[1] MASSACHUSETTS GEN HOSP,CHILDRENS NEUROL SERV,BOSTON,MA 02114
[2] BOSTON CITY HOSP,NEUROPATHOL SERV,BOSTON,MA 02118
关键词
D O I
10.1007/BF00692698
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:55 / 63
页数:9
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共 43 条
[1]   NEUROPATHOLOGICAL FINDINGS IN PHENYL-PYRUVIC OLIGOPHRENIA (PHENYL-KETONURIA) [J].
ALVORD, EC ;
STEVENSON, LD ;
VOGEL, FS ;
ENGLE, RL .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1950, 9 (03) :298-310
[2]  
[Anonymous], MODERN NEUROLOGY
[3]   PHENYLKETONURIA PRESENTING AN INTERMITTENT PROGRESSIVE COURSE [J].
BECHAR, M ;
BORNSTEIN, B ;
ELIAN, M ;
SANDBANK, U .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1965, 28 (02) :165-+
[4]  
BEDNAR B, 1967, CS PATOL, V3, P221
[5]  
Benda, 1952, DEV DISORDERS MENTAT
[6]   EFFECT OF EXCESS PHENYLALANINE AND OF OTHER AMINO ACIDS ON BRAIN DEVELOPMENT IN INFANT RAT [J].
CHASE, HP ;
OBRIEN, D .
PEDIATRIC RESEARCH, 1970, 4 (01) :96-&
[7]  
CLARK JTR, 1969, CAN J BIOCH, V47, P29
[8]  
Conel J.L., 1939, POSTNATAL DEV HUMAN
[9]  
COQUET M, 1944, MONATSCHR PSYCH NEUR, V109, P135
[10]   THE PATHOLOGICAL REPORT OF A CASE OF PHENYLPYRUVIC OLIGOPHRENIA [J].
CORSELLIS, JAN .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1953, 16 (03) :139-143