MHC CLASS-II DEFICIENCY - REPORT OF THE 1ST ITALIAN CASE

被引:0
作者
CANDOTTI, F
PORTA, F
MAZZOLARI, E
LANFRANCHI, A
NOTARANGELO, LD
BRAGA, S
CANIGLIA, M
UGAZIO, AG
机构
来源
RIVISTA ITALIANA DI PEDIATRIA-ITALIAN JOURNAL OF PEDIATRICS | 1992年 / 18卷 / 02期
关键词
IMMUNODEFICIENCY; MHC CLASS-II; BONE MARROW TRANSPLANTATION;
D O I
暂无
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
MHC class II deficiency (MHC Cl II Def.) is a rare primary combined immunodeficiency with severe evolution. Despite treatment with allogeneic bone marrow trasplantation (BMT), complete immunologic reconstitution has been rarely achieved in contrast to the results of BMT in other immunodeficiency. We describe the first italian patient with MHC Cl II Def. unsuccessfully treated with haploidentical BMT.
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页码:223 / 227
页数:5
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