L-CARNITINE THERAPY IN ISOVALERIC ACIDEMIA

被引：84

作者：

ROE, CR

MILLINGTON, DS

MALTBY, DA

KAHLER, SG

BOHAN, TP

机构：

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1984年 / 74卷 / 06期

关键词：

D O I：

10.1172/JCI111657

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：2290 / 2295

页数：6

共 17 条

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[8] APPLICATION OF HIGH-RESOLUTION FAST ATOM BOMBARDMENT AND CONSTANT B-E RATIO LINKED SCANNING TO THE IDENTIFICATION AND ANALYSIS OF ACYLCARNITINES IN METABOLIC DISEASE [J].

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[9] METABOLIC RESPONSE TO CARNITINE IN METHYLMALONIC ACIDURIA - AN EFFECTIVE STRATEGY FOR ELIMINATION OF PROPIONYL GROUPS [J].

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[10] L-CARNITINE ENHANCES EXCRETION OF PROPIONYL COENZYME-A AS PROPIONYLCARNITINE IN PROPIONIC ACIDEMIA [J].

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JOURNAL OF CLINICAL INVESTIGATION, 1984, 73 (06) :1785-1788

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