ANOMALOUS ORIGIN OF THE LEFT MAIN PULMONARY-ARTERY FROM THE ASCENDING AORTA ASSOCIATED WITH DIGEORGE-SYNDROME

被引:36
作者
DODO, H
ALEJOS, JC
PERLOFF, JK
LAKS, H
DRINKWATER, DC
WILLIAMS, RG
机构
[1] UNIV CALIF LOS ANGELES,DEPT MED,LOS ANGELES,CA 90024
[2] UNIV CALIF LOS ANGELES,DEPT SURG,LOS ANGELES,CA 90024
[3] UNIV CALIF LOS ANGELES,DIV MED CARDIOL,LOS ANGELES,CA
[4] UNIV CALIF LOS ANGELES,DEPT PEDIAT CARDIOL,LOS ANGELES,CA
[5] UNIV CALIF LOS ANGELES,DIV CARDIOTHORAC SURG,LOS ANGELES,CA
[6] UNIV CALIF LOS ANGELES,CTR ADULT CONGENITAL HEART DIS,LOS ANGELES,CA
关键词
D O I
10.1016/S0002-9149(99)80788-7
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We place on record 2 infants with the DiGeorge syndrome and anomalous origin of the left pulmonary artery from the ascending aorta. We postulate that: (1) embryogenesis of anomalous origin of the left pulmonary artery from the ascending aorta might be due to the persistent fifth aortic arch connecting both arterial systems; (2) an anomalous pulmonary artery arising from the ascending aorta is part of the aortic arch abnormality accompanied by normal conotruncal septation; and (3) in the DiGeorge syndrome, cardiac anomalies that originate from the conotruncus or aortic arch, or both, may have the same embryologic mechanisms. © 1995 Excerpta Medica, Inc. All rights reserved.
引用
收藏
页码:1294 / 1295
页数:2
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