AORTIC-VALVE REPLACEMENT IN CARDIAC OCHRONOSIS

被引:9
作者
KIM, YI [1 ]
DAENEN, W [1 ]
机构
[1] UNIV HOSP GASTHUISBERG,DEPT CARDIAC SURG,HERESTR 49,B-3000 LOUVAIN,BELGIUM
关键词
ALKAPTONURIA; OCHRONOSIS; AORTIC VALVE REPLACEMENT;
D O I
10.1016/1010-7940(92)90139-O
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Two patients with generalized ochronosis developed cardiovascular symptoms related to cardiac ochronosis with aortic valvular stenosis. One patient with a transvalvular pressure gradient of 150 mm Hg underwent emergency aortic valve replacement. The other patient with a transvalvular pressure gradient of % mm Hg underwent successful elective aortic valve replacement. Cardiac ochronosis is a rare disease that might be encountered, with the typical signs, during an elective, planned cardiac operation. The most frequent presenting feature of this disease seems to be aortic valvular stenosis.
引用
收藏
页码:625 / 626
页数:2
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