Marked Retroperitoneal Lymphadenopathy in Hairy Cell Leukemia: A Case Report

被引:9
作者
Shackelford, R. E. [1 ]
Heldmann, M. [1 ]
Eskandari, F. [1 ]
Joshi, N. [1 ]
Browning, J. [1 ]
Maxwell, N. [1 ]
Coteligam, J. [1 ]
机构
[1] LSU Hlth Shreveport, Dept Pathol, 1501 Kings Highway, Shreveport, LA 71130 USA
来源
CASE REPORTS IN ONCOLOGY | 2013年 / 6卷 / 03期
关键词
Hairy cell leukemia; Retroperitoneal lymphadenopathy;
D O I
10.1159/000355434
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Hairy cell leukemia (HCL) is uncommonly associated with lymphadenopathy, while retroperitoneal lymphadenopathy is extremely uncommon. We report on a patient with a 12-year history of HCL who developed painless jaundice and ascites, accompanied by positional discomfort with persistent nausea. Computed tomography examination revealed 2 large retroperitoneal masses, which at autopsy consisted of HCL with focally intermixed pancreatic and peripancreatic tissue. Lymphadenopathy was not identified above the diaphragm or below the aortic bifurcation. No vasculitis or an unusual HCL histology was identified. As previous reports, our findings suggest that HCL with massive lymphadenopathy has a specific site predilection, but it is not necessarily accompanied by vasculitis or an unusual histology. (C) 2013 S. Karger AG, Basel
引用
收藏
页码:493 / 496
页数:4
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