Anesthetic management of Shah-Waardenburg syndrome: Experience of two cases and review of literature

被引：3

作者：

Ambi, Uday S. ^{[1
]}

Adarsh, E. S. ^{[1
]}

Hatti, Ramesh ^{[2
]}

Samalad, Vijaymahantesh ^{[2
]}

机构：

[1] SN Med Coll & Hosp, Dept Anaesthesiol, Bagalkot 587102, Karnataka, India

[2] SN Med Coll & Hosp, Surg, Bagalkot, Karnataka, India

来源：

SAUDI JOURNAL OF ANAESTHESIA | 2012年 / 6卷 / 02期

关键词：

Anesthesia; Shah-Waardenburg syndrome; white forelock;

D O I：

10.4103/1658-354X.97034

中图分类号：

R614 [麻醉学];

学科分类号：

100217 ;

摘要：

Waardenburg syndrome (WS) is a rare autosomally inherited and genetically heterogeneous disorder of neural crest cell development. Literature regarding the anesthetic management of these cases is limited. We present 2 cases of Shah-Waardenburg syndrome and discuss them in the context of review of previously published cases.

引用

页码：172 / 174

页数：3

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