CHARACTERISTIC CLINICAL-FEATURES IN A CASE OF FULMINANT SUBACUTE SCLEROSING PANENCEPHALITIS

被引:25
作者
TAKAYAMA, S [1 ]
IWASAKI, Y [1 ]
YAMANOUCHI, H [1 ]
SUGAI, K [1 ]
TAKASHIMA, S [1 ]
IWASAKI, A [1 ]
机构
[1] SAITAMA CTR NEUROL & PSYCHIAT,DIV NEUROL,YONO,JAPAN
关键词
FULMINANT SSPE; SUBACUTE SCLEROSING PANENCEPHALITIS; VISUAL DISTURBANCE; MYOCLONUS; PERIODIC EEG COMPLEX; MAGNETIC RESONANCE IMAGING; IMAGING; MRI; GENICULATE BODY;
D O I
10.1016/0387-7604(94)90049-3
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 12-year-old girl with fulminant subacute sclerosing panencephalitis (SSPE) without myoclonic jerk and periodic EEG complexes is reported. She presented with blurred vision, fell into a coma after 2 weeks and died within 4 months. Magnetic resonance image (MRI) disclosed high intensity lesions in the lateral geniculate bodies, when the patient initially complained of blurred vision. Reviewing the cases of fulminant SSPE in the literature, more than half of the patients showed blurred vision or visual agnosia as an initial symptom. Most of those patients were female and rapidly deteriorated to a comatose state within 2 weeks. Based on the MRI study of the present patient, we speculate that the initial visual impairment in such patients can be attributed to the involvement of the lateral geniculate body.
引用
收藏
页码:132 / 135
页数:4
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