SPONTANEOUS COLONIC ISCHEMIA IN A PATIENT WITH RILEY-DAY SYNDROME

被引：2

作者：

APPLEGATE, KE ^{[1
]}

SARGENT, SK ^{[1
]}

机构：

[1] DARTMOUTH COLL,HITCHCOCK MED CTR,DEPT RADIOL,LEBANON,NH 03756

来源：

PEDIATRIC RADIOLOGY | 1995年 / 25卷 / 04期

关键词：

D O I：

10.1007/BF02011113

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Familial dysautonomia, or Riley-Day syndrome, is a hereditary disturbance in the autonomic and peripheral sensory nervous systems, first described by Riley, Day, and colleagues in 1949 [1, 2]. Previous reports of myocardial infarction and avascular necrosis in bone suggest that these patients are at risk for ischemia at certain organ sites [3, 4]. We report a case of spontaneous colonic ischemia and stricture which resulted in colocutaneous fistula formation and eventual colonic resection in a child with Riley Day syndrome.

引用

页码：312 / 313

页数：2