MORPHOLOGICAL AND BIOCHEMICAL CONFIRMATION OF GRAY PLATELET SYNDROME IN 2 SIBLINGS

被引:31
作者
BERNDT, MC
CASTALDI, PA
GORDON, S
HALLEY, H
MCPHERSON, VJ
机构
[1] UNIV SYDNEY,WESTMEAD CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
[2] UNIV NEWCASTLE,FAC MED,NEWCASTLE,NSW 2308,AUSTRALIA
[3] SYDNEY HOSP,DEPT HEMATOL,SYDNEY,NSW 2000,AUSTRALIA
来源
AUSTRALIAN AND NEW ZEALAND JOURNAL OF MEDICINE | 1983年 / 13卷 / 04期
关键词
D O I
10.1111/j.1445-5994.1983.tb04488.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:387 / 390
页数:4
相关论文
共 23 条
[1]  
BERNDT MC, 1981, J BIOL CHEM, V256, P59
[2]  
BRADFORD MM, 1976, ANAL BIOCHEM, V72, P248, DOI 10.1016/0003-2697(76)90527-3
[3]  
BRETONGORIUS J, 1981, AM J PATHOL, V102, P10
[4]   EVIDENCE FOR A PLATELET MEMBRANE DEFECT IN THE MYELOPROLIFERATIVE SYNDROMES [J].
CASTALDI, PA ;
BERNDT, MC ;
BOOTH, W ;
GREGORY, C ;
BULL, H ;
GREAVES, M .
THROMBOSIS RESEARCH, 1982, 27 (05) :601-609
[5]   THROMBIN-INDUCED PLATELET-AGGREGATION IS MEDIATED BY A PLATELET PLASMA MEMBRANE-BOUND LECTIN [J].
GARTNER, TK ;
WILLIAMS, DC ;
MINION, FC ;
PHILLIPS, DR .
SCIENCE, 1978, 200 (4347) :1281-1283
[6]  
GARTNER TK, 1981, BLOOD, V58, P153
[7]   QUANTITATIVE-ANALYSIS OF PLATELET MEMBRANE-GLYCOPROTEINS - EFFECT OF PLATELET WASHING PROCEDURES AND ISOLATION OF PLATELET DENSITY SUB-POPULATIONS [J].
GEORGE, JN ;
THOI, LL ;
MORGAN, RK .
THROMBOSIS RESEARCH, 1981, 23 (1-2) :69-77
[8]   BIOCHEMICAL-STUDIES OF 2 PATIENTS WITH THE GRAY PLATELET SYNDROME - SELECTIVE DEFICIENCY OF PLATELET ALPHA GRANULES [J].
GERRARD, JM ;
PHILLIPS, DR ;
RAO, GHR ;
PLOW, EF ;
WALZ, DA ;
ROSS, R ;
HARKER, LA ;
WHITE, JG .
JOURNAL OF CLINICAL INVESTIGATION, 1980, 66 (01) :102-109
[9]   PLATELET FACTOR-4 - INHIBITOR OF COLLAGENASE [J].
HITIHARPER, J ;
WOHL, H ;
HARPER, E .
SCIENCE, 1978, 199 (4332) :991-992
[10]   CAUSES FOR THE DISCREPANCIES IN THE MEASUREMENTS OF FACTOR-VIII ANTIGEN [J].
HOWARD, MA ;
HAU, L ;
PERKIN, J ;
THOMAS, KB ;
FIRKIN, BG ;
KOUTTS, J .
THROMBOSIS RESEARCH, 1980, 19 (1-2) :63-72