FATTY-ACID OXIDATION IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH INHERITED DISORDERS OF FATTY-ACID METABOLISM - STUDIES ON THE SPECIFICITY OF ACYL-COA DEHYDROGENASES

被引:3
作者
CHALMERS, RA [1 ]
ENGLISH, N [1 ]
机构
[1] MRC,CLIN RES CTR,HARROW HA1 3UJ,MIDDX,ENGLAND
关键词
D O I
10.1042/bst0150489
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:489 / 489
页数:1
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[31]   MICROSOMAL FATTY-ACID SYNTHETASE COUPLED TO ACYL-COA REDUCTASE IN EUGLENA-GRACILIS [J].
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KOLATTUKUDY, PE .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1973, 158 (01) :411-420
[32]   ABNORMAL-METABOLISM OF VERY LONG-CHAIN FATTY-ACID IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH ADRENOLEUKODYSTROPHY [J].
CHEN, WW ;
LUE, N ;
MURALIDHARAN, VB ;
KISHIMOTO, Y ;
MOSER, HW .
JOURNAL OF CELL BIOLOGY, 1982, 95 (02) :A453-A453
[33]   INCORPORATION OF CIS-PARINARIC ACID, A FLUORESCENT FATTY-ACID, INTO SYNAPTOSOMAL PHOSPHOLIPIDS BY AN ACYL-COA ACYLTRANSFERASE [J].
HARRIS, WE ;
STAHL, WL .
BIOCHIMICA ET BIOPHYSICA ACTA, 1983, 736 (01) :79-91
[34]   FATTY-ACID BETA-OXIDATION IN LEUKOCYTES FROM CONTROL SUBJECTS AND MEDIUM-CHAIN ACYL-COA DEHYDROGENASE DEFICIENT PATIENTS [J].
WANDERS, RJA ;
IJLST, L .
BIOCHIMICA ET BIOPHYSICA ACTA, 1992, 1138 (01) :80-84
[35]   REGULATION OF FATTY-ACID SYNTHESIS IN HUMAN SKIN FIBROBLASTS - INHIBITION OF FATTY-ACID SYNTHESIS BY FREE FATTY-ACIDS [J].
JACOBS, RA ;
MAJERUS, PW .
JOURNAL OF BIOLOGICAL CHEMISTRY, 1973, 248 (24) :8392-8401
[36]   THE MEASUREMENT OF CARNITINE AND ACYL-CARNITINES - APPLICATION TO THE INVESTIGATION OF PATIENTS WITH SUSPECTED INHERITED DISORDERS OF MITOCHONDRIAL FATTY-ACID OXIDATION [J].
BHUIYAN, AKMJ ;
JACKSON, S ;
TURNBULL, DM ;
AYNSLEYGREEN, A ;
LEONARD, JV ;
BARTLETT, K .
CLINICA CHIMICA ACTA, 1992, 207 (03) :185-204
[37]   THE CHANGING FACE OF DISORDERS OF FATTY-ACID OXIDATION [J].
VOCKLEY, J .
MAYO CLINIC PROCEEDINGS, 1994, 69 (03) :249-257
[38]   COMPLEMENTATION ANALYSIS OF FATTY-ACID OXIDATION DISORDERS [J].
MOON, A ;
RHEAD, WJ .
JOURNAL OF CLINICAL INVESTIGATION, 1987, 79 (01) :59-64
[39]   FATTY-ACID OXIDATION DISORDERS - OVERVIEW AND INTRODUCTION [J].
SAUDUBRAY, JM ;
BONNEFONT, JP ;
SCHWARTZ, G ;
BRIVET, M ;
VASSAULT, A ;
DEMAUGRE, F ;
RABIER, D ;
CHARPENTIER, C .
AMERICAN JOURNAL OF HUMAN GENETICS, 1991, 49 (04) :52-52
[40]   ADRENOLEUKODYSTROPHY - ELEVATED C26 FATTY-ACID IN CULTURED SKIN FIBROBLASTS [J].
MOSER, HW ;
MOSER, AB ;
KAWAMURA, N ;
MURPHY, J ;
SUZUKI, K ;
SCHAUMBURG, H ;
KISHIMOTO, Y .
ANNALS OF NEUROLOGY, 1980, 7 (06) :542-549