FATTY-ACID OXIDATION IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH INHERITED DISORDERS OF FATTY-ACID METABOLISM - STUDIES ON THE SPECIFICITY OF ACYL-COA DEHYDROGENASES

被引：3

作者：

CHALMERS, RA ^{[1
]}

ENGLISH, N ^{[1
]}

机构：

[1] MRC,CLIN RES CTR,HARROW HA1 3UJ,MIDDX,ENGLAND

来源：

BIOCHEMICAL SOCIETY TRANSACTIONS | 1987年 / 15卷 / 03期

关键词：

D O I：

10.1042/bst0150489

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：489 / 489

页数：1

共 8 条

[1]

Chalmers R, 1983, BIOCHEM SOC T, V11, P724

[2] URINARY-EXCRETION OF L-CARNITINE AND ACYLCARNITINES BY PATIENTS WITH DISORDERS OF ORGANIC-ACID METABOLISM - EVIDENCE FOR SECONDARY INSUFFICIENCY OF L-CARNITINE [J].

CHALMERS, RA ;

ROE, CR ;

STACEY, TE ;

HOPPEL, CL .

PEDIATRIC RESEARCH, 1984, 18 (12) :1325-1328

[3] THE USE OF FAST-ATOM-BOMBARDMENT MASS-SPECTROMETRY TO IDENTIFY AND STUDY URINARY ACYLCARNITINES IN DISORDERS OF ORGANIC-ACID METABOLISM [J].

CHALMERS, RA ;

TRACEY, BM ;

STACEY, TE ;

CHENG, KN ;

MADIGAN, MJ ;

LAWSON, AM .

BIOCHEMICAL SOCIETY TRANSACTIONS, 1986, 14 (05) :967-969

[4]

CHALMERS RA, 1987, IN PRESS J INHER S2, V10

[5] GENETIC DEFICIENCY OF MEDIUM-CHAIN ACYL COENZYME-A DEHYDROGENASE - STUDIES IN CULTURED SKIN FIBROBLASTS AND PERIPHERAL MONONUCLEAR LEUKOCYTES [J].

COATES, PM ;

HALE, DE ;

STANLEY, CA ;

CORKEY, BE ;

CORTNER, JA .

PEDIATRIC RESEARCH, 1985, 19 (07) :671-676

[6] FLUOROMETRIC ASSAY OF ACYL-COA DEHYDROGENASES IN NORMAL AND MUTANT HUMAN-FIBROBLASTS [J].

FRERMAN, FE ;

GOODMAN, SI .

BIOCHEMICAL MEDICINE, 1985, 33 (01) :38-44

[7] FATTY ACYL-COA DEHYDROGENASE-DEFICIENCY - ENZYME MEASUREMENT AND STUDIES ON ALTERNATIVE METABOLISM [J].

GREGERSEN, N .

JOURNAL OF INHERITED METABOLIC DISEASE, 1984, 7 :28-32

[8] OXIDATION OF FATTY-ACIDS IN CULTURED FIBROBLASTS - A MODEL SYSTEM FOR THE DETECTION AND STUDY OF DEFECTS IN OXIDATION [J].

SAUDUBRAY, JM ;

COUDE, FX ;

DEMAUGRE, F ;

JOHNSON, C ;

GIBSON, KM ;

NYHAN, WL .

PEDIATRIC RESEARCH, 1982, 16 (10) :877-881

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