METABOLIC RESPONSE TO CARNITINE IN METHYLMALONIC ACIDURIA - AN EFFECTIVE STRATEGY FOR ELIMINATION OF PROPIONYL GROUPS

被引：118
作者：
ROE, CR
HOPPEL, CL
STACEY, TE
CHALMERS, RA
TRACEY, BM
MILLINGTON, DS
机构：
[1] CLIN RES CTR, MRC, PAEDIAT RES GRP, WATFORD RD, HARROW HA1 3UJ, MIDDX, ENGLAND
[2] DUKE UNIV, MED CTR, DIV PEDIAT METAB, DURHAM, NC 27710 USA
[3] CASE WESTERN RESERVE UNIV, SCH MED, VET ADM MED CTR, DEPT PHARMACOL, CLEVELAND, OH 44106 USA
[4] CASE WESTERN RESERVE UNIV, SCH MED, DEPT MED, CLEVELAND, OH 44106 USA
[5] UNIV N CAROLINA, DEPT ENVIRONM HLTH SCI & ENGN, CHAPEL HILL, NC 27514 USA
来源：
ARCHIVES OF DISEASE IN CHILDHOOD | 1983年 / 58卷 / 11期
关键词：
D O I：
10.1136/adc.58.11.916
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
引用
收藏
页码：916 / 920
页数：5
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