SUCCESSFUL TREATMENT OF RECURRENT THROMBOTIC THROMBOCYTOPENIC PURPURA WITH PLASMAPHERESIS AND VINCRISTINE

被引:0
作者
VANGOOL, S [1 ]
BROCK, P [1 ]
VANLAER, P [1 ]
VANDAMMELOMBAERTS, R [1 ]
PROESMANS, W [1 ]
CASTEELSVANDAELE, M [1 ]
机构
[1] UNIV HOSP GASTHUISBERG,DEPT PAEDIAT,B-3000 LOUVAIN,BELGIUM
关键词
THROMBOTIC THROMBOCYTOPENIC PURPURA; PLASMAPHERESIS; VINCRISTINE;
D O I
暂无
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
An adolescent girl with severe thrombotic thrombocytopenic purpura (TTP) remained in a critical condition after 3 weeks of combined treatment with antiplatelet drugs, plasma infusions and plasma exchange. The introduction of vincristine resulted in gradual improvement and eventual complete remission which lasted for 2 years. When she relapsed, immediate improvement was observed with the combined treatment of plasmapheresis and vincristine. She has now been in complete remission again for 10 months. It is suggested that plasmapheresis plus vincristine should be used as the initial treatment for children with TTP.
引用
收藏
页码:517 / 519
页数:3
相关论文
共 22 条
[1]   IMPROVED SURVIVAL IN THROMBOTIC THROMBOCYTOPENIC PURPURA HEMOLYTIC UREMIC SYNDROME - CLINICAL-EXPERIENCE IN 108 PATIENTS [J].
BELL, WR ;
BRAINE, HG ;
NESS, PM ;
KICKLER, TS .
NEW ENGLAND JOURNAL OF MEDICINE, 1991, 325 (06) :398-403
[2]  
Byrnes J J, 1980, Adv Intern Med, V26, P131
[3]   TREATMENT OF THROMBOTIC THROMBOCYTOPENIC PURPURA WITH PLASMA [J].
BYRNES, JJ ;
KHURANA, M .
NEW ENGLAND JOURNAL OF MEDICINE, 1977, 297 (25) :1386-1389
[4]   EARLY PLASMAPHERESIS IN PATIENTS WITH THROMBOTIC THROMBOCYTOPENIC PURPURA [J].
DOUZINAS, EE ;
MARKAKIS, K ;
KARABINIS, A ;
MANDALAKI, T ;
BILALIS, D ;
FESSAS, P .
CRITICAL CARE MEDICINE, 1992, 20 (01) :57-61
[5]   INEFFICACY OF INTRAVENOUS IMMUNOGLOBULIN IN PATIENTS WITH LOW-RISK THROMBOTIC THROMBOCYTOPENIC PURPURA/HEMOLYTIC-UREMIC SYNDROME [J].
FINAZZI, G ;
BELLAVITA, P ;
FALANGA, A ;
VIERO, P ;
BARBUI, T .
AMERICAN JOURNAL OF HEMATOLOGY, 1992, 41 (03) :165-169
[6]   TREATMENT OF THROMBOTIC THROMBOCYTOPENIC PURPURA WITH VINCRISTINE [J].
GUTTERMAN, LA ;
STEVENSON, TD .
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1982, 247 (10) :1433-1436
[7]  
GUTTERMAN LA, 1992, HEMOLYTIC UREMIC SYN, P513
[8]   HIGH-DOSE INTRAVENOUS IMMUNOGLOBULIN AS THERAPY FOR THROMBOTIC THROMBOCYTOPENIC PURPURA [J].
KOLODZIEJ, M .
AMERICAN JOURNAL OF THE MEDICAL SCIENCES, 1993, 305 (02) :101-102
[9]   THROMBOTIC THROMBOCYTOPENIC PURPURA [J].
MURPHY, WG ;
MOORE, JC ;
WARKENTIN, TE ;
HAYWARD, CPM ;
KELTON, JG .
BLOOD COAGULATION & FIBRINOLYSIS, 1992, 3 (05) :655-659
[10]   RESPONSE TO PLASMA-EXCHANGE AND SPLENECTOMY IN THROMBOTIC THROMBOCYTOPENIC PURPURA - A 10-YEAR EXPERIENCE AT A SINGLE INSTITUTION [J].
ONUNDARSON, PT ;
ROWE, JM ;
HEAL, JM ;
FRANCIS, CW .
ARCHIVES OF INTERNAL MEDICINE, 1992, 152 (04) :791-796